Prune Belly Syndrome Flashcards
1
Q
What is the triad of prune belly syndrome?
A
- abdominal muscle deficiency
- anomalous development of the urinary tract
- bilateral cryptocordism
2
Q
Hypotheses for the aetiology of prune belly syndrome
A
- urinary tract obstruction
- primary mesodermal developmental defect
3
Q
Category 1 features of prune belly syndrome
A
- Oligohydramnios
- Potter facies
- severe pulmonary hypoplasia
- severe renal dysplasia
- only in males
4
Q
Category 2 features of prune belly syndrome
A
- typical external features without Potter facies
- dilatation on the urinary tract with less severe dysplasia
5
Q
Category 3 features of prune belly syndrome
A
- external features mild or incomplete
- mildly dilated urinary tract with normal renal parenchyma
