Peutz-Jeghers syndrome

Question 1

Peutz-Jeghers syndrome is an?

Answer 1

autosomal dominant c

Question 2

Characteristic of Peutz-Jeghers syndrome

Answer 2

numerous hamartomatous polyps in the gastrointestinal tract. I

Question 3

Clinical features of peutz jeghers syndrome ?

Answer 3

pigmented freckles on the lips, face, palms and soles

hamartomatous polyps in the gastronintestinal tract (mainly small bowel) - because if this small bowel obstruction common - due to intussusception

Question 4

Is peutz jeghers syndrome associated with gastrointestinal cancer

Answer 4

The hamartas themselves do not have malignant evolution however associated with other gastrointestinal tract cancer which the risk for is very high