Parenchymal restrictive lung disorders Flashcards
Pulmonary fibrosis- Risk
- Exposure to radiation for lung or breast cancer
- Radiation pneumonitis
Pulmonary fibrosis- Sx
- Asymtomatic to slowly progressive dyspnea
- Bibasilar inspiratory crackles
- Reduced lung volume
Pulmonary fibrosis- Dx
CXR- obliteration of normal lung markings, dense interstitial and pleural fibrosis, tenting of diaphragm
Sarcoidosis- Risk
- Women in 3rd-4th decade- black women
- Granulomatous inflammation of lung
Sarcoidosis- Sx
- Insidious onset of arthralgia, fever & dyspnea on exertion, anorexia
- Erythema nodosum, skin lesions, pigment changes
- Skin, eye, nerve involvement
- Parotid gland enlargement, hepatosplenomegaly, lymphadenopathy
- No crackles
Sarcoidosis- Dx
- CXR: Bilateral hilar adenopathy and parenchymal involvement
- Histology indicating noncaseating graulomas + clinical presentation
- Elevated ESR, ACE,
Sarcoidosis- Tx
- Prednisone x 6 months
Coal worker’s pneumoconiosis- Risk
- Occupational inhalation of coal dust
- Cigarette smoke
Coal worker’s pneumoconiosis- Sx
- Asymptomatic
- Normal PFT
- Progressive, massive fibrosis of lungs due to macrophages ingesting inhaled coal dust
Coal worker’s pneumoconiosis- Dx
CXR: Small opacities in upper lung field
Coal worker’s pneumoconiosis- Tx
Supportive tx
Asbestosis- Risk
- Nodular, interstial fibrosis due to long term asbestos exposure
- Cigarette smoking
Asbestosis- Sx
- Progressive dyspnea
- Inspiratory crackles
- Clubbing & cyanosis
- Lower lung involvement
- Reduced diffusion, restrictive defects on PFT
Asbestosis- Dx
-CXR: linear streaking at base, honeycomb changes, opacities, pleural calcification
Asbestosis- Tx
None
Hypersensitivity pneumonitis- Risk
Exposure to antigen- hay, humidifies, birds, sawdust, bark, mushrooms
Hypersensitivity pneumonitis- Sx
- Acute illness 4-8 hrs following exposure
- Bibasilar crackles, tachypnea, tachycardia, cyanosis
Hypersensitivity pneumonitis- Dx
- PFT: Restrictive pattern
- ABG: Hypoxemia
- CXR: small, nodular densities sparing apaches and bases
- Bronchoscopy
Hypersensitivity pneumonitis- Tx
Corticosteroids
Byssinosis- Risk
- Cotton textile industry workers
- Occupational asthma
Byssinosis- Sx
- Chest tightness, cough & dyspnea 1-2 hrs after returning to work after several days off
Byssinosis- Dx
- Symptomatic presentation plus changes in lung function- spirometery
Byssinosis- Tx
- Tx as asthma
- Protective equipment