Paeds: CF

Question 1

Main dietetic aims for Cystic Fibrosis (PAEDS):

Answer 1

Main dietetic aims for Cystic Fibrosis (PAEDS):
* Bone health maintenance (at risk of osteoporosis due to digestive issues)
* Optimum vitamin levels
* Support growth & development
* Control malabsorption symptoms
* Normal eating behaviours
* Maintenance of blood sugar in cystic fibrosis related diabetes

Question 2

Main nutritional concerns in Cystic Fibrosis

Answer 2

Main nutritional concerns in CYSTIC FIBROSIS:
* Malnutrition risk is HIGH
* Malabsorption
* No enzymes from pancreas: Pancreatic enzyme replacement
* Salt: Higher requirements
* Fluid: Needed to loosen secretions

Question 3

What is Cystic Fibrosis?

Answer 3

Cystic Fibrosis is an autosomal recessive inheritance disease caused by genetic mutation which results in a faulty CFTR gene that causes a build-up of thick, sticky mucus on cell surfaces. The effects of the disease vary for Cystic Fibrosis sufferers, but they often experience issues with their respiratory and digestive systems

Question 4

What are common problems in Cystic Fibrosis?

Answer 4

Common problems in Cystic Fibrosis:
* Weight loss
* Undernutrition
* Excess gained weight (older children and adults)

Question 5

What IS NOT recommended for Cystic Fibrosis sufferers with pancreatic enzyme insufficiency?

Answer 5

It IS NOT recommended for Cystic Firbrosis sufferers with pancreatic enzyme insufficiency to have a fat restriction because this may lead to reduced energy intake in a group of individuals that are already at risk of malnutrition. Fat restriction is only recommended in the minority of patients who are taking PERT but steatorrhoea cannot be controlled.

Question 6

Infants with CF