paediatric orthopaedics, neuromuscular conditions Flashcards

1
Q

complex needs

A

a child with multiple and complex disabilities has at least two different types of severe or profound impairment such that no one professional/ discipline has monopoly on assessment and management

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2
Q

complex exceptional needs

A
learning and mental functions 
communication 
motor skills 
self care 
hearing 
vision 
Definition: child<19
severe impairment in 4 categories together with enteral or parenteral feeding
OR
severe impairment  in 2 and ventilation 
AND impairments sustained for more than 6 mths ongoing
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3
Q

cerebral palsy

A

permanent and non-progressive motor disorder due to brain damage before birth or during the first 2 years of life.

The lesion is static but the clinical picture is not.

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4
Q

causes of cerebral palsy

A

Prenatal: placental insufficiency, toxaemia, smoking, alcohol, drugs, infection such as toxoplasmosis, rubella, CMV and herpes type II (TORCH)

Perinatal: prematurity (most common), anoxic injuries, infections, kernicterus, erythroblastosis fetalis

Postnatal: infection (CMV, rubella), head trauma

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5
Q

classification

A

Spastic (pyramidal system, motor cortex)
Athetoid (extrapyramidal system, basal ganglia)
Ataxia (cerebellum and brainstem)
Rigid (basal ganglia and motor cortex)
Hemiballistic
Mixed (combination of spasticity and athetosis)

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6
Q

anatomical

A

Monoplegia (one limb involved)
Hemiplegia (one side of the body)
Diplegia (lower limbs)
Quadriplegia or total body involvement

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7
Q

diagnosis 1

A
spasticity
lack of voluntary control
weakness
poor coordination
sensory impairment
persistence of primitive reflex: parachute, tonic neck
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8
Q

diagnosis 2

A

dynamic contractures
fixed muscle contractures
fixed contractures with joint subluxation/ dislocation and secondary bone changes

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9
Q

management

A
motor
sensory
cognitive problems
epilepsy
feeding difficulties
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10
Q

orthopaedics priorities

A

spine
hip
feet
torsional lower limb probs

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11
Q

system goals

A

sitting balance
standing posture
gait

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12
Q

functional problems

A
keeping clean
no longer able to stand
feet too deformed to fit in spints and skin is breaking down
in pain
knees too sore to walk
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13
Q

prerequisites of normal gait

A
Stability in stance
Clearance in swing
Preposition of foot
Adequate step length
Energy conservation
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14
Q

muscle actions

A

concentric

  • shortening
  • power generation
  • acceleration

eccentric

  • controlled lengthening
  • power absorption
  • deceleration
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15
Q

spine in CP

A

scoliosis common
surgery to
maintain seating and respiratory function

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16
Q

Hip

A

normal at birth
but displacement later on
surgical intervention crucial

17
Q

clinical assessment

A

hamstring tightness

pelvic obliquity

18
Q

GMFCS

A

gross motor function classification system.
higher grading
Xray+ Annual examination

19
Q

interventions

A
-Posture management 
Physiotherapy
Seating
-Spasticity management
General
Baclofen
Diazepam
Specific
Botulinum toxin
Surgery
-Deformity management
Soft tissue release-
Adductors
Hamstrings
Bony realignment-
Varus Derotation Osteotomy
Pelvic Osteotomy
20
Q

multidisciplinary effort

A
wheelchair services
physiotherapy
education support
orthotics
occupational therapy
social work
opthalmology
audiology
orthopaedics
community paediatrics
21
Q

Spina bifida

A
Failure to close neural tube
Folic acid protective 400mcg/day
Occulta – benign
Meningocele
Myelomeningocele
Encephalocele
Anencephaly
22
Q

myelomeningocele

A
Hydrocephaly
Chiari II malform
Tethered cord
Urinary tract problems
latex allergy
learning disability
23
Q

muscular dystrophy

A

FSH, DMD, BMD, Limb girdle, Myotonic, Emery Dreifus, Oculo-pharyngeal

Muscle Bx, DNA, Blood enzymes & EMG
Cardiomyopathy…Respiratory failure

24
Q

Duchenne

A
Sex linked recessive
Failure to make dystrophin
1 in 3000 males
Proximal weak 4yoa
‘pseudohypertrophy’
Wheelchair by 12yoa
Most get scoliosis
Surgery indicated
25
Q

Becker

A

Same gene, ltd but poor dystrophin
Milder
Later (adolescent) onset
Wheelchair by 30yoa

26
Q

MD

A
shoulders and arms held back
belly sticks out due to weak belly
knees may bend back
thick lower leg muscles (mostly fat)
foot drop and tip toe contractures