Nutrition & Metabolic: Acute Porphyrias Flashcards
1
Q
What are the acute porphyrias?
A
Hereditary disorders of haem biosynthesis; prevalance of about 1 in 75000
2
Q
Where can clinical advice regarding the safety of drugs in acute porphyrias be sought?
A
BNF and then the National Acute Prorphyria Service or from the UK Porphyria Medicines Information Service.
3
Q
How can moderate, severe or unremitting acute porphyria crises be treated?
A
Haem arginate via short intravenous infusion.
4
Q
Can gabapentin be used in acute porphyria?
A
Yes
