Neuro tumors

Question 1

port-wine stains

Answer 1

sturge weber

Question 2

nevus flammeus

Answer 2

sturge weber

Question 3

sequelae of sturge weber

Answer 3

glaucoma, seizures, hemiparesis, mental retardation

Question 4

ipsilateral leptomeningeal angioma, pheochromocytoma

Answer 4

sturge weber

Question 5

inheritance pattern of sturge weber

Answer 5

sporadic

Question 6

what is the clinical presentation of tuberous sclerosis

Answer 6

HAMARTOMAS:
hamartomas in CNS, adenoma sebaceum, mitral regurgitation, ash-leaf spots, cardiac rhabdomyoma, autosomal dominant, mental retardation, renal angiomyolipoa, seizures

Question 7

ash-leaf spots

Answer 7

tuberous sclerosis

Question 8

inheritance pattern of tuberous sclerosis

Answer 8

AD

Question 9

lisch nodules

Answer 9

NF1 (von recklinghausen)

Question 10

nf1 inheritance

Answer 10

AD

Question 11

where is NF1 gene located

Answer 11

chromosome 17

Question 12

optic gliomas, pheochromocytomas

Answer 12

NF1

Question 13

cavernous hemangiomas in skin, mucosa, organs, bilateral renal cell carcinoma, hemangioblastoma in retina, brain ste , cerebellum, pheochromocytoma

Answer 13

von hippel lindau

Question 14

cafe au lait spots

Answer 14

NF1

Question 15

inheritance of von hippel lindau

Answer 15

AD

Question 16

von hippel lindau has what mutated gene?

Answer 16

VHL gene, chromosome 3, tumor suppressor

Question 17

iris hamartomas

Answer 17

nF1 (lisch nodules)

Question 18

most common primary brain tumor

Answer 18

glioblastoma multiforme (astrocytoma grade IV)

Question 19

butterfly glioma

Answer 19

glioblastoma

Question 20

lobulated mass near corpus callosum

Answer 20

glioblastoma

Question 21

psuedopalisading pleomorphic tumor cells

Answer 21

glioblastoma multiforme

Question 22

2nd most common primary brain tumor

Answer 22

meningioma

Question 23

whorled pattern, psammoma bodies

Answer 23

meningioma

Question 24

cell type in meningioma

Answer 24

arachnoid cells

Question 25

third most common primary brain tumor

Answer 25

schwannoma

Question 26

bilateral acoustic schwannoma is found in what disease process?

Answer 26

NF2

Question 27

NF2 presents with…

Answer 27

bilateral acoustic schwannoma

Question 28

S100 positive

Answer 28

schwannoma

Question 29

tumor found at cerebellopontine angle

Answer 29

schwannoma

Question 30

CN assocaited with schwannoma

Answer 30

CN VIII

Question 31

treatment for schwannoma

Answer 31

usually resectable or treated with stereotactic radiosurgery

Question 32

fried egg appearance

Answer 32

oligodendroglioma

Question 33

slow growing tumor in frontal lobes

Answer 33

oligodendroglioma

Question 34

chicken wire capillary pattern

Answer 34

oligodendrioglioma

Question 35

bitemporal hemianopia

Answer 35

pituitary adenoma (commonly prolactinoma)

Question 36

rosenthal fibers

Answer 36

eosinphilic, pilocytic

Question 37

cell type of medulloblastoma

Answer 37

neuroectodermal

Question 38

homer-wright rosettes

Answer 38

medulloblastoma

Question 39

small blue cells

Answer 39

medulloblastoma

Question 40

tumor most commonly found in 4th ventricle

Answer 40

ependymoma

Question 41

perivascular psuedorosettes

Answer 41

ependymoma

Question 42

rod-shaped blepharoplasts (basal ciliary bodies)

Answer 42

ependymoma

Question 43

childhood tumor that can cause bitemporal hemianopia

Answer 43

craniopharyngioma

Question 44

where is craniopharyngeoma derived from

Answer 44

rathke’s pouch

Question 45

most common childhood supratentorial tumor

Answer 45

craniopharyngeoma