HIRSCHSPRUNG'S DISEASE Flashcards
GI pedia disorders
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Congenital aganglionic megacolon, also called Hirschsprung disease, is characterized by persistent constipation resulting from partial or complete intestinal obstruction of mechanical origin.
absence of gangion cells whish are responsible for peristalsis
HIRSCHSPRUNG’S DISEASE
Hirschsprung disease results from the absence of enteric neurons within the ___ and ____ of the rectum and/or colon.
myenteric and submucosal plexus
s/sx during NEONATAL PERIOD
Failure to pass meconium stool after 24 hours.
s/sx during EARLY CHILDHOOD
- Ribbon like stool
- Constipation
- Foul smelling stool
- Diarrhea
After 6 weeks - Gradual bloating of stomach
- Vomiting with bile
- Loss of Apetite
- Delayed Growth
s/sx during EARLY CHILDHOOD
- Ribbon like stool
- Constipation
- Foul smelling stool
- Diarrhea
- After 6 weeks
- Gradual bloating of stomach
- Vomiting with bile
- Loss of Apetite
- Delayed Growth
s/sx during EARLY CHILDHOOD
- Ribbon like stool
- Constipation
- Foul smelling stool
- Diarrhea
- After 6 weeks
- Gradual bloating of stomach
- Vomiting with bile
- Loss of Apetite
- Delayed Growth
Dx. Test
- Barium Enema
- ABD. X-ray
- Rectal Biopsy
- Rectal Manometry
Surgical MNGT.
- Colostomy after 2=3 months
- Anastomosis
Diet
Low residue
High calorie
Type of Stool
Ascending colon
watery
Type of Stool
Transverse colon
Mushy
Type of Stool
Descending colon
Semi-solid
Type of Stool
Sigmoid colon
hard stool
