bernard-soulier syndrome (BSS)

Question 1

Hemorrhagiparous Thrombolytic Dystrophy

Answer 1

Bernard-soulier syndrome (bss)

Question 2

rare platelet membrane receptor defect

Answer 2

Bernard-soulier syndrome (bss)

Question 3

platelet’s ability to adhere is decreased

Answer 3

Bernard-soulier syndrome (bss)

Question 4

defect of the GPIb-IX-V gene complex

Answer 4

Bernard-soulier syndrome (bss)

Question 5

this membrane protein complex facilitates two major platelet functions:
a. binding of platelets to vWF and thus adhesion to the subendothelial space, and
b. the ability of thrombin at low concentrations to activate platelets

Answer 5

Gp1b-IX-V gene complex

Question 6

giant platelet cells

Answer 6

Bernard-soulier syndrome (bss)

Question 7

peripheral blood smear that can show giant
platelets and thrombocytopenia

Answer 7

Bernard-soulier syndrome (BSS)

Question 8

Platelet transfusions

Answer 8

Bernard-Soulier (Giant Platelet)
Syndrome