AP

Question 1

Wagner-Meissner bodies

Answer 1

Seen in neurofibromas (especially diffuse type)

Question 2

% of NF1 pts who develop MPNST

Answer 2

3-5%

Question 3

optic nerve pilocytic astrocytoma seen in NF__

Answer 3

NF1

Question 4

Bilateral acoustic schwannomas seen in NF_

Answer 4

NF2

Question 5

S100 staining in neurofibroma vs MPNST

Answer 5

s100 stronger in neurofibroma

weaker/patchy in MPNST

Question 6

Bednar tumor

Answer 6

DFSP + melanin pigment

Question 7

soft tissue tumor that may have “pulmonary edema” pattern

Answer 7

myxoid liposarcoma

Question 8

perineurium stains + with

Answer 8

EMA

Question 9

positive stains in perineurioma

Answer 9

EMA

Claudin 1

Question 10

Evans tumor also called

Answer 10

Low-grade fibromyxoid sarcoma

Question 11

stain positive in low-grade fibromyxoid sarcoma

Answer 11

MUC4

Question 12

TFE3+ soft tissue tumor

Answer 12

alveolar soft part

Question 13

Triton tumor

Answer 13

MPNST + rhabdomyoblasts

Question 14

fibrous dysplasia + myxoma =

Answer 14

Mazabraud syndrome

Question 15

doege-potter syndrome

Answer 15

hypoglycemia with solitary fibrous tumor

Question 16

myxoinflammatory fibroblastic tumor

Answer 16

same as Dr. Weiss’s RS and virocyte-like tumor

occurs on dorsum of foot