3rd BIMONTHLY RECALLS

Question 1

What is the most common cause
of acute renal failure in
children?

a. Hemolytic-Uremic Syndrome
b. Henoch-Schonlein Purpura
Nephritis
c. Goodpasture Syndrome
d. Chronic Tubulointerstitial
Nephritis

Answer 1

a. Hemolytic-Uremic Syndrome

Question 2

Chronic granulomatous disease
shows the following clinical
features EXCEPT:

a. Dermatitis
b. Otitis media
c. Acute suppurative infection
d. Hepatomegaly with abscess

Answer 2

c. Acute suppurative infection

Question 3

This syndrome is caused by
mutations in the PTX2
transcription gene.

a. Hall-Pallister syndrome
b. Hypogammaglobulinemia
c. Reiger syndrome
d. Ritter’s syndrome

Answer 3

c. Reiger syndrome

Question 4

One of the following is associated
with increased risk of developing
chronic uveitis among children
with JRA?

a. ANA titer
b. Rheumatoid factor
c. Elevated ESR, CRP
d. Hypergammaglobulinemia

Answer 4

a. ANA titer

Question 5

A life threatening form of
hemophagocytic lymphohistiocytosis is commonly associated with this deficiency.

a. Chediak Higashi Syndrome
b. Leukocyte Adhesion Defect
c. Wisckott Aldrich Syndrome
d. Severe Combined
Immunodeficiency

Answer 5

a. Chediak Higashi Syndrome

Question 6

One of the following laboratory
parameters is specific for SLE in
children:

a. ANA
b. Anti-dsDNA
c. ANti-Smith antibody
d. C-reactive proteins

Answer 6

c. ANti-Smith antibody

Question 7

Mutations in this gene cause
septo-optic dysplasia:

a. HESX1
b. LHX3
c. LHX4
d. PTX2

Answer 7

a. HESX1

Question 8

The initial single most important
laboratory test for a child with
short stature is

a. CBC
b. urinalysis
c. Serum electrolytes
d. x-ray of L hand for bone aging

Answer 8

d. x-ray of L hand for bone aging

Question 9

Shawl sign is seen in which of the
following rheumatic diseases of
childhood?

a. Juvenile dermatomyositis
b. Henoch-Schِnlein purpura
c. Systemic lupus
erythematosus
d. Systemic-onset juvenile
idiopathic arthritis

Answer 9

a. Juvenile dermatomyositis

Question 10

Rita, an 11-year-old female with history of fatigue, malaise, and progressive muscle weakness, accompanied by low-grade fevers and scaly, red plaques are found across the knuckles, she is not able to sit up from a supine
position. Laboratory exams showed elevated muscle enzymes (ALT, AST, LDH, CPK, and aldolase), EMG abnormalities: fasciculations, needle insertion irritability, and high-frequency discharges. What do you think is the complication for this disease?

a. calcinosis
b. infections
c. avascular necrosis
d. myocardial infarction

Answer 10

a. calcinosis

Question 11

One of the following is not a
minor criteria in the diagnosis of
Juvenile Systemic Sclerosis:

a. Hepatomegaly
b. Right sided heart failure
c. Gastroesophageal reflux
d. Pulmonary hypertension

Answer 11

a. Hepatomegaly

Question 12

Linear IgG on immunofluorescence is found in this particular renal disease that manifests as acute glomerulonephritis.

a. Ig A Nephropathy
b. Goodpasture Syndrome
c. Poststreptococcal Glomerulonephritis
d. Rapidly Progressive Glomerulonephritis

Answer 12

b. Goodpasture Syndrome

Question 13

The rheumatic diseases of
childhood are characterized by
autoimmunity and inflammation,
which may be localized or
generalized. Which of the
following is the classical rheumatic
disease of childhood :

a. Scleroderma
b. Bechet syndrome
c. Juvenile rheumatoid arthritis
d. Sjogren syndrome

Answer 13

c. Juvenile rheumatoid arthritis

Question 14

Definitive diagnosis of short
stature is the provocative test.
One of the following is not
included :

a. Insulin
b. arginine
c. leucine
d. glucagon

Answer 14

c. leucine

Question 15

Bruton tyrosine kinase protein is
commonly associated with this
type of immunodeficiency.

a. Chediak Higashi Syndrome
b. Leukocyte Adhesion Defect
c. Chronic Granulomatous
Disease
d. X-linked Agammaglobulinemia

Answer 15

d. X-linked Agammaglobulinemia

Question 16

Leukocyte adhesion defect will
have a significant leukocytosis of:

a. >22,000
b. >23,000
c. >24,000
d. >25,000

Answer 16

d. >25,000

Question 17

One of the closest differential
diagnosis for infants patients
presenting with colds, cough and
wheezing that is often interpreted
as bronchial asthma?

a. Foreign body aspiration
b. Bronchopulmonary dysplasia
c. Pediatric community
acquired pneumonia
d. Viral bronchiolitis

Answer 17

???

Question 18

The accelerated phase in Chediak-
Higashi Syndrome is characterized
by the following features EXCEPT:

a. High fever
b. Thrombocytopenia
c. Lympocytopenia
d. Shortened bleeding time

Answer 18

d. Shortened bleeding time??

Question 19

What is the common visceral
manifestation of patients with
scleroderma?

a. Dyspnea
b. Dysphagia
c. Failure to thrive
d. Raynaud phenomenon

Answer 19

a. Dyspnea

Question 20

It is a complication of Atopic
dermatitis that presents with
itching, burning, tearing and
copious mucoid discharge; it
involves the eyes and is usually
bilateral with Trantas dots or
Giant papillae may be present

a. Exfoliative dermatitis
b. Atopic keratoconjunctivitis
c. Keratoconus
d. Allergic conjunctivitis

Answer 20

b. Atopic keratoconjunctivitis

Question 21

Which of the following manifests
with hypertension in 70% of
cases:

a. Ig A nephropathy
b. Goodpastures Syndrome
c. Poststreptococcal GN
d. Rapidly progressive
glomerulonephritis

Answer 21

c. Poststreptococcal GN

Question 22

One of the current goals of
treatment in the latest Allergic
Rhinitis and its Impact on Asthma
ARIA guidelines is to promote safe
effective prevention and relief of
symptoms. This specific measure
is a very helpful method to reduce
the symptoms of allergic
disease:

a. Bed linens and blankets
washed 3 times a week
b. Allow pets at home
c. Keep windows open to
facilitate exit of pollens and
dust
d. Allergen proof encasings

Answer 22

d. Allergen proof encasings

Question 23

This is the most common
radiologic finding in the early
stages of juvenile idiopathic
arthritis (JIA):

a. fusion of C1-4
b. erosions of bony articular surfaces
c. normal bone x-ray
d. evidence of bony proliferation
e. periarticular osteopenia

Answer 23

e. periarticular osteopenia

Question 24

The predominant sites of
involvement of atopic dermatitis
in infants is/are:

a. Chest and umbilical area
b. Digits and armpits
c. Flexor surface of the
extremities
d. Cheeks, extensor surface of extremities

Answer 24

d. Cheeks, extensor surface of extremities

Question 25

This particular diagnostic tool is
commonly used in Hemolytic
Uremic Syndrome,

a. Renal Ultrasound
b. Kidney Biopsy
c. Clinical Criteria
d. Stool exam

Answer 25

??? c. Clinical Criteria