vascular tumors

Question 1

PHACES Syndrome

Answer 1

posterior fossa, hemangioma, arterial anomalies (internal carotid/cerebral a.), cardiac issues (coarctation of aorta), eye issues (cataracts), sternal cleft or supra umbilical raphe

Tx: MRI/MRA followed by oral propranolol

Question 2

LUMBAR/SACRAL

Answer 2

LUMBAR : lower body hemangioma, urogenital anomalies, myelopathy, bony deformity, anorectal malformation, renal anomalies

SACRAL : spinal dysraphism, anogenital anomalies, cutaneous anomalies, renal and anal anomalies, angioma of lumbosacral area

Tx: topical propranolol +/- MRI or ultrasound IFF hemangioma crosses midline of lower spine

Question 3

Neonatal hemangiomatosis

Answer 3

benign > 5 limited to skin

diffuse > 5 with internal involvement (often liver), may lead to liver failure or high output heart failure

Tx topical propranolol

Question 4

Kasabach-Merritt phenomenon

Answer 4

ndcnajn

Question 5

Vascular malformations includes: capillary malformations

Answer 5

sdjvfns

Question 6

Capillary malformation

Answer 6

several syndromes

Question 7

Sturge Weber Syndromes

Answer 7

capillary malformation in V1 distribution