Tetralogy of Fallot

Question 1

What are the 4 components with tetralogy of fallot?

Answer 1

right ventricular hypertrophy, pulmonic stenosis (causing right ventricular outflow obstruction), ventricular septal defect, overriding aorta

Question 2

Is tetrology of fallot a cyanotic or acyanotic disease?

Answer 2

cyanotic

Question 3

How old are these patients when they present with cyanosis from tet of fallot?

Answer 3

2-10 days

Question 4

What will be heard on auscultation?

Answer 4

single second heart sound, systolic ejection murmur at left upper sternal border (maybe radiating to the back)

Question 5

What are some other associations with tet of fallot?

Answer 5

cleft palate, hypospadias, skeletal malformations

Question 6

Does oxygen improve this cyanosis?

Answer 6

no

Question 7

What test can be done to check for tet of fallot?

Answer 7

Hyperoxia test–give 100% FiO2 for 10 minutes then get ABG…if paO2 is

Question 8

What is immediate tx for tet of fallot?

Answer 8

give prostaglandin E1 to open the ductus

Question 9

What can be done to treat tet of fallot until a full surgical repair can be done?

Answer 9

temporize with Blalock-Taussig shunt (BT shunt)

Question 10

What is the most appropriate tx for a tet spell?

Answer 10

beta blocker