Scleroderma

Question 1

Describe the definition of Scleroderma

Answer 1

It is a systemic autoimmune disease

Question 2

Describe the aetiology and pathophysiology Scleroderma

Answer 2

Pathophysiology: It is characterized by increased synthesis of collagen, which can lead to sclerosis.

Question 3

List the main signs and symptoms for Scleroderma

Answer 3

Skin: healed pitted ulcers on the fingertips.
Cardiovascular: scarring, arrhythmia, pericarditis
Pulmonary: fibrosis, hypertension, dyspnea and chest pain
Digestive: acid re-flux, constipation and diarrhea

Question 4

Describe the responses/benefits of EXP for people w/Scleroderma

Answer 4

Counteracts: muscle weakening effects and aerobic deconditioning effects of disease; EXT: is likely to slow down or reverse other systemic effects

Question 5

Describe the contraindications to EXP for people w/Scleroderma

Answer 5

Refrain from exercise if there is any evidence of cardiac or pulmonary distress, i.e. chest pain, dyspnoea

Question 6

What are the recommendations and modifications for people w/Scleroderma?

Answer 6

Aerobic training: 20 mins at 70% of VO2peak, if possible increase to 80%
Resistance: 4 sets of 8-12 repetitions
Aim to take care of skin