Sclerodema

Question 0

What are the types of scleroderma?

Answer 0

• localized scleroderma
• limited systemic sclerosis (C.R.E.S.T)
• diffuse systemic sclerosis (generalized)

Question 1

Define scleroderma

Answer 1

Autoimmune disease of the connective tissue characterized by thickening of skin, fascia, tendon sheaths and organs of the body.

Question 2

What is mauskopf?

Answer 2

Pucked appearance with difficulty opening the mouth. (Mouse headed appearance)

Question 3

What are some of the causes if scleroderma?

Answer 3

Idiopathic

Heredity

Environment

Question 4

Define calcinosis…

Answer 4

Formation of tiny calcium deposits on the skin usually overlying honey prominences such as elbows, knees or fingers.

Question 5

What is esophageal dysmotility?

Answer 5

Poor function of muscles of lower 2/3 of esophagus. Leads to to widening of esophagus causing reflux of stomach acid leading to heartburn, inflammation and scarring of stomach lining.

Question 6

Tiny red blotches caused by dilated capillaries appearing on the face, hands n mouth defines which feature of Limited Systemic Sclerosis?

Answer 6

Telangiectasia.

Question 7

Which type of scleroderma is rapidly progressive, with frequent renal n pulmonary involvement?

Answer 7

Diffuse Systemic Sclerosis

Question 8

What is the hallmark feature of diffuse systemic sclerosis?

Answer 8

Skin lesions on the trunk of the body

Question 9

What medication is used to treat calcinosis?

Answer 9

Colchicine (gout medication)

Question 10

Limited systemic sclerosis is often referred to as CREST syndrome as it takes the name from first letter of conditions most common symptoms.

True / False?

Answer 10

True.

C-calcinosis
R-Raynaud's phenomenon
E-esophageal dysmom
S-sclerodactyly
T-telangiectasia

Question 11

Localized thickening of the skin over the fingers and toes with puffy shiny appearance describes which symptom?

Answer 11

Sclerodactyly

Question 12

What are the types of scleroderma?

Answer 12

• localized
• limited
• diffuse

Question 13

-rapid progression, renal and pulmonary involvement
-skin lesions on trunk of body
-affected esophagus, congestive cardiac failure
-malignant hypertension, lung tissue fibrosis
-death
Are all presentations/ manifestations of Limited scleroderma. True / False?

Answer 13

False.

Diffuse scleroderma.

Question 14

Protein is encouraged as aid in treating scleroderma.

True / False?

Answer 14

False.

Advised against high protein diets as they are hard on kidneys.

Question 15

Best position for treatment in scleroderma is prone.

True / False?

Answer 15

False.

Supine semi reclined
comfort n systemic complications
-shorter treatments (45mins ideal)

Question 16

What are some contraindications to treating scleroderma?

Answer 16

• excessively long/aggressive treatment
• cold hydro on hands esp if Raynauds present
• direct tq on inflamed joints
• position for comfort, hypertension n cardiac failure
• GERD modifications

Question 17

Patients are advised to avoid chewing gum as his may exacerbate TMJ n stimulate gastric acids thus triggering GERD.

True / False?

Answer 17

True.