RESTRICTIVE CARDIOMYOPATHY

Question 1

Definition

Answer 1

Infiltration of the myocardium results in a rigid ventricle leading to an impaired diastolic filling

Question 2

Causes (6)

Answer 2

1- Amyloidosis
2- Sarcoidosis
3- Haemochromatosis
4- Scleroderma
5- Carcinoid syndrome
6- Chemotherapy and radiation

Question 3

Investigation (2)

Answer 3

1- ECG, CXR, and Echo are abnormal and have nonspecific features
2- Diagnosis made by cardiac catheterization showing pressure changes and biopsy may be taken for histological diagnosis

Question 4

Management

Answer 4

No specific treatment and prognosis is poor, however diuretics and vasodilators may be used for symptomatic relief