Pulmonary Fibrosis Flashcards
1
Q
What is idiopathic pulmonary fibrosis?
A
Formation of scar tissue in lungs with no known cause
2
Q
What is the most common interstitial lung disease?
A
Idiopathic pulmonary fibrosis
3
Q
How does IPF present?
A
Dyspnoea, dry cough, bibasal crackles
4
Q
What is the gold standard investigation?
A
High resolution CT
5
Q
What does a high res CT look like?
A
Ground glass appearance
6
Q
What drugs would you prescribe?
A
Pirfenidone, nintedanib
7
Q
What non-pharmacological management would you start?
A
Smoking cessation, physiotherapy, vaccines up to date
8
Q
What is the last resort management?
A
Lung transplantation
