PT management of lifelong conditions Flashcards
Not a single disease; Encompasses all forms of arthritis that demonstrate onset prior to 16 years of age, last longer than 6 weeks, and have an unknown origin; Diagnosis is based on clinical presentation
Juvenile idiopathic arthritis (JIA)
What is the pathogenesis of JIA?
Pathogenesis is not well understood; however, likely:
- Autoimmune inflammatory condition
- Activated by an external trigger
- In a genetically pre-disposed individual
What is the most common type of JIA?
Oligoarthritis
- low-grade inflammation in four or fewer joints, most commonly affects the knee; early childhood onset peaks 2-4 years
What are the types of JIA?
- Systemic arthritis - throughout childhood; F=M
- Oligoarthritis - early childhood, peaks 2-4 years; F»>M
- Rh (+) polyarthritis - late childhood or adolescence; F»M
- Rh (-) polyarthritis - peaks 2-4 and 6-12 years; F»M
- Enthesitis-related arthritis - peaks late childhood or adolescence; M»F
- Psoriatic arthritis - peaks 2-4 and 9-11 years; F»M
- undifferentiated arthritis
What are the S and S of JIA?
- Joint swelling, pain, stiffness
- Morning stiffness** - Indicates active disease; Hallmark sign
- Muscle atrophy; weakness; poor muscle endurance
- Acute or chronic iridocyclitis (typically in oligoarticular): asymptomatic inflammation of the eye that may lead to functional blindness. Treated with corticosteroids; Need to make sure child is seeing opthamologist
- Systemic manifestations - Severe in systemic JIA; Mild to moderate in polyarticula
- Decreased joint ROM secondary to soft tissue contracture
- Fatigue
- Decreased aerobic capacity; impaired exercise tolerance
- Growth abnormalities
- Osteopenia or osteoporosis- Increased with long term corticosteroid use
- Gait Impairments
- Difficulty with ADLs
- Activity & Participation Restrictions
What is the PT management of JIA?
- Control inflammation
- Preserve joint structure and function - Prevent secondary impairments at the joint
- Promote participation
- Educate the family and child
What is the instrument commonly used to assess JIA?
CHAQ
- looks at all 3 levels of ICF model
- .143 indicates clinically important change from PT
What pain rating scales are good for assessing pain in children with JIA?
- Oucher scale
- Faces
- Rating scale
- poker chip tool
What does PT intervention include?
- Address ROM (AROM, no stretching)
- Increase strength (isometric strengthening)
- Improve cardiovascular fitness - Decrease fatigue
- Promote appropriate gross motor skill
- Educate the family on the benefits of maintaining ROM and participating in aerobic activity as well as signs of systemic disease
- Provide family-centered care
- Use of modalities to control pain and maximize ROM
- Educate on the benefits of sleep
- Guided imagery for relaxation, distraction
What surgical procedures are used in JIA?
- Soft Tissue Release - Common sites: hip flexor, ITB, hamstrings; Role of PT: preserve gained ROM through functional activities, splinting and ROM exercises
- Supracondylar osteotomy
Arthrodesis - Epiphysiodesis to prevent/correct leg length discrepencies
- Post-Operative PT: Increase strength, ROM; Gait training; Educate on postoperative precautions set by physician
What are the prognostic indicators for JIA?
- Overall, improving functional outcomes over the past decade
- Negative:
1. Hip involvement and polyjoint involvement in systemic and oligo JIA within the first year of disease presence
2. Rheumatoid Factor (+) - Positive:
1. Oligo JIA has best prognosis for joint preservation and function
2. Onset of symptoms >9 years of age in males
3. Early and effective treatment
Nonprogressive disorder characterized by multiple joint contractures and muscle weakness or imbalance; Incidence: 1 in 3000 to 4000; Suspected cause is a suspension of movement during the fetal periods of development, which results in contractures; Etiology is not well understood, but likely a genetic link; Association with other disease processes where the motor unit, including the anterior horn cells, is impaired.
Arthrogryposis Multiplex Congenita (AMC)
What are the characteristics of AMC?
- Cylindric-shaped joints that lack creases
- Rigid joints, significant contractures
- Joint dislocation, especially at the hips
- Atrophy or absence of entire muscle groups
- Intact sensation, though deep tendon reflexes (DTRs) may be diminished or absent
- Symmetric presentation
What is typical presentation of AMC?
- Shoulder internal rotation
- Elbow flexion or extension
- Wrist flexion with ulnar deviation
- Hip flexion with internal rotation or a frog-legged posture
- Knee flexion or extension
- Equinovarus at the feet
What is the appropriate PT management of AMC?
- Passive stretching - NOT forceful– could result in joint damage; Maintain range with splints
- Positioning
- Serial casting and splinting
- Strengthening
- Promote development of motor skills - Mobility (Usually through power mobility)
- Post-operative rehabilitation
- Adaptive Equipment prescription