Physiotherapy in CF Flashcards

1
Q

What does physio for CF include?

A
  • Airway clearance
  • Inhalation therapy
  • Exercise to maximise CR fitness, strength & bone density
  • Advice on continence issues & pelvic floor exercises
  • Thoracic mobility
  • Postural advice
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2
Q

What are the features of airway clearance in CF?

A

Commences at diagnosis

  • Individualised
  • Choice of modality depends on many factors (age, compliance, social factors, financial situation, severity)
  • Techniques used separately or in combination
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3
Q

What are the aims of airway clearance?

A
  • Clear airway of secretions
  • Improve ventilation
  • Lessen effects of infection
  • Avoid deterioration of breathing mechanics
  • Preserve pulmonary function in the long term
  • Improve QOL
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4
Q

What airway clearance techniques are used in CF?

A
  • Postural drainage
  • Modified postural drainage
  • Percussion/vibrations
  • ACBT (blowing games)
  • PEP (FRC focus)
  • Oscillating PEP
  • Autogenic drainage
  • High frequency chest wall oscillation
  • Interpulmonary percussive ventilation
  • Exercise
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5
Q

What are the precautions for coughing in CF?

A
  • Repeated cough can damage airway walls
  • Only clears central section of the lung
  • Need ACT to get secretions from deeper lung segments up to be cleared by cough
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6
Q

What does MCC require in CF?

A
  • Adequate systemic hydration
  • Cilia sit in layer of mucus, dehydration leads to sticker mucus & poor cilia function
  • Second half of treatment really important for mucus that has to travel
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7
Q

What are the features of inhalation therapy in CF?

A
1. Optimise timing with airway clearance
• Pre-physio: bronchodilators, mucolytics, pulmozyme
• Post-physio: antibiotics, pulmozyme
2. Equipment selection important
- Use slow inspirations
- Mouthpiece better than face mask
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8
Q

What is dornase alpha?

A
  • Enzyme that cuts up the strands of RNA released with cell death & found in thick sticky mucus
  • Thins secretions
  • Very expensive
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9
Q

How should pulmozymes be timed with ACTs?

A

Absence of strong evidence to indicate that one timing regimen is better than another

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10
Q

What has research found regarding hypertonic saline in CF?

A
  • Improves FVC & FEV1
  • Decreases infective exacerbation rate
  • Decreases hospitalisation rate
  • Safe to introduce in acute exacerbation for adults
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11
Q

What is the role of Mannitol in CF?

A
  • Sugar alcohol that acts as an osmotic agent
  • Developed into bronchitol for use as a dry powder inhalation in the lungs
  • Large RCT showed improvement in lung function following 6 months use
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12
Q

What is a TOBI Podhaler?

A
  • Option for delivering anti-pseudomonal antibiotic to the lungs
  • Equal efficacy to nebulised solution
  • 25% of the time, increased patient satisfaction, increased adherence, reduced exacerbations
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13
Q

What are the benefits of exercise in CF?

A
  • Improved CV fitness
  • Improved muscle strength
  • Improved QOL
  • Improved core stability & thoracic mobility
  • Improved prognosis
  • Improved lung function
  • Improve airway clearance
  • Potential effect on bone mineral density & CF related diabetes
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14
Q

What does exercise testing in CF involve?

A
  • Regular testing recommended at leat anually
  • Cardiopulmonary exercise testing (VO2 max)
  • Field tests (6MWT, 3 min step test, modified shuttle walk test)
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15
Q

What is the purpose of exercise testing in CF?

A
  • Measure of disease severity/progress
  • Assist in exercise prescription
  • Quantify level of exercise limitation
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16
Q

What has research found regarding exercise participation in CF?

A
  • Parental involvement extremely important in early years
  • Limiting passive entertainment a huge challenge
  • Reduction in exercise participation after puberty, especially in girls (CF & general population
  • Children with CF do significantly less PA than well peers
17
Q

What are some of the programs for increasing PA in children with CF?

A
  • Fitbit program

- Give me 5 for kids

18
Q

What are some of the musculoskeletal issues in CF?

A
  • Spinal pain: Associated with reduced QOL, sleep disturbance, anxiety, depression, ADLs
  • Low bone mineral density: Accelerates during adolescence & early adulthood
  • Fractures: Due to low BMD, OP & chronic steroid risk
  • Thoracic kyphosis
  • CF arthropathy: Includes joint pain, long bone pain, joint effusions
19
Q

What is the prevalence of urinary incontinence in CF?

A
  • 22-64% in girls/women (compared to 12-30% normal)

- Important to determine cause (stress, overactive bladder, urge, poor voiding habits, constipation etc)

20
Q

What does the treatment of incontinence in women with CF involve?

A
  • Qualified continence physio
  • Exercise, e stim, biofeedback & bladder training
  • Produces significant improvements in pelvic floor strength, reduction in leakage & QOL
21
Q

What is the role of physio in treating inpatients?

A
  • Intensive physiotherapy for respiratory exacerbations
  • Airway clearance +/- exercise
  • Detailed review and fine-tuning
22
Q

What is the role of physio in treating outpatients?

A
  • Educate
  • Regular review of program & techniques
  • Collect sputum
  • Support compliance & get to know them
  • Function well within MDT
23
Q

Who is provided with education?

A
  • Initially with parents & family: Role of physio, assist with clinical expectations
  • Then with child/adolescent
24
Q

Why is it important to keep the family & child educated?

A

Adherence correlates with optimism, family function disease knowledge & parental education