peutz-jeghers syndrome

Question 1

what is peutz-jeghers syndrome

Answer 1

autosomal dominant condition characterised by numerous hamartomatous polyps in the GI tract

Question 2

features of peutz-jeghers syndrome

Answer 2

hamartomatous polyps in GI tract (small bowel)
- causing small bowel obstruction due to intussusception
- GI bleeding
pigmented lesions on lips, oral mucosa, face, palms and soles

Question 3

management of peutz-jeghers syndrome

Answer 3

conservative unless complications develop