Pediatrics- Complications of Infants Flashcards
What is phenylketonuria
PKU is an inherited metabolic disorder in which the newborn likes the enzyme phenylalanine hydroxylase
This enzyme converts phenylanine and essential amino acid into Trysonie
The lack of this enzyme leads to the accumulation of phenylaline in the newborns, bloodstream and tissues, which causes cognitive impairment
What is the key prevention of PKU in newborns?
Identification of clients in the reproductive years, who have disorder mess it here, to strict dietary guidelines from three months before conception throughout pregnancy
How often do patients with KPK you have to get there phenylalanine levels monitored
1 to 2 times per week throughout pregnancy
Who gets screen for PKU?
All newborns buy bullets brought protein usually within the first two days of birth
Expected findings in a newborn with PKU
Growth failure
Frequent vomiting
Irritability
Musty odor in urine
Blue eyes very fair skin light blonde hair
When is the blood spot analysis performed to check for PKU?
After the newborn has ingested, a source of protein, usually within two days of birth
What is nursing care of PKU?
Focuses on dietary intake
Dietary restrictions, as soon as PKU was diagnosed, or within 7 to 10 days of birth
Please patient on formula low in phenylalanine
Breast feed contains enzyme so I might not be possible
What should be the intake for a newborn with PKU?
20 to 30 mg phenylalanine per kilogram of body weight per day
Call is level between two and eight
What are complications of PKU?
Cognitive impairment
Hyper activity with erratic behavior
Bizarre behavior
Headbanging
Arm biting
Spasticity
What is meningocele/ myelomenigiocele
Spina bifida,
Neural tube defects that are present at birth in affect the CNS and spine
Occur when neural tube fails to close during the third and fourth week of embryonic development
What is meningiocele
Protrusion of saclike says that contains meninges in spinal fluid
What is myelomenigiocele
Upper Tution of saclike says that contains meninges, spinal fluid, and a portion of the spinal cord and nerves
What allergy do you have to assess for in spina bifida
Latex
What are manifestations of increased intracranial pressure
Hi bitch cry
Lethargic
Vomiting
Bothering fontanelles
Widen, cranial, suture lines
Increase head circumference
What is necrotizing enterocolitis?
An inflammatory disease of the G.I. Makossa caused by a Soumia or hypoxia. She may result in death of mucosal sell, leading to necrotic patches that interfere with digestion.
Respecters for necrotizing enterocolitis
Prematurity
Respiratory distress
Intrauterine growth restriction
Receiving internal feeds
G.I. vascular compromise
Physical assessment of a patient with necrotizing enterocolitis
Abdominal distention
Bloody stools
Periods of apnea
Hypotension
Poor feeding
What is a diagnostic procedure for necrotizing enterocolitis?
Abdominal x-rays
Look for sausage shaped dilation of intestine
Characterize soapsuds appearance of intestinal wall due to air infiltration
Free air and abdominal cavity, if perforation has occurred
Nursing care for a patient with necrotizing enterocolitis
Prevention with hold feedings for 24 to 48 hours
Discontinue all feedings
Insert NG tube
Measure abdominal girth
Scereal abdominal x-rays
Removal of necrotize portion of bowel
Temporary colostomy
What is respiratory distress syndrome?
Results of surfactant deficiency in the lungs, characterized by pour gas exchange, and ventiltory failure
What does surfactant
Phospholipid that assist in Alviola expansion keeps alveoli from collapsing and allows Gas exchange to occur
What is atelectasis?
Collapsing a portion of the lungs