Lecture 31 - Congenital Heart Disease in Adults

Question 1

_______ Syndrome describes late-onset cyanosis from reversal of Left-to-Right shunt when pulmonary pressure increases enough.

Answer 1

Eisenmenger

Question 2

ASDs that form from Ostium primum are associated with cleft ______ or _____ valves, which should make sense being that the Ostium Primum is lower on the Atrial septum. The EKG of these patients may show incomplete _____. Remember that these patients’ heart sounds will show a wide split ____ that will not resolve on inspiration (the pulmonic valve will continue to close late), and most often presents in the ___ to ___ decade of life.

Answer 2

Cleft Mitral or Tricuspid valves.

Incomplete RBBB

Wide split S2

3rd to 4th

Question 3

Know that adults with VSD may present with a palpable _____, which will not be true for ASDs. Also look for harsh ________ murmur.

Answer 3

Thrill

Holosystolic

Question 4

PDA is more common in premature births and in people who were born at high _____ (think [O2]). Remember it is the breathing in of O2 that causes closure of the PDA. PDAs will present as _______ type murmurs.

Answer 4

Altitude

Machine type (sounds like washing machine)

Question 5

For adults with Aortic Coartication, look for low pressure in the _____ extremities vs the _____ extremities. Keep in mind it is 3x more likely in MALES, and it is associated with ______ (what kind?) aortic valve.

Answer 5

Lower extremities

Upper extremities

Bicuspid

Question 6

Williams Syndrome (look for blue starry eyes, wide mouth with small teeth spaced apart) is associated with Supravalvular ______ stenosis.

Answer 6

Aortic

Question 7

Noonan’s Syndrome (patients with wooly hair and Pectus sternal deformity) is associated with ______ stenosis.

Answer 7

Pulmonic