Know It Pt.9 Flashcards
The etiology of HCM is ______but may be transmitted by an __________ with ____ penetrance
Idiopathic; autosomal dominant gene; variable
ASH stands for?
Asymmetric septal hyper trophy
SAM stands for?
Systolic anterior motion
IHSS stands for?
Idiopathic hypertrophic subaortic stenosis
HOCM stands for?
Hypertrophic obstructive cardiomyopathy
IHSS is?
A) SAM & HCM
B)SAM
C)ASH
D)SAM & ASH
D
HOCM is?
A) SAM & HCM
B)SAM
C)ASH
D)SAM & ASH
A
Which cardiomyopathy is autosomal dominant?
A) dialated
B) Infiltrative
C)Hypertrophic
D)restrictive
C
HCM has _____ dysfunction
Diastolic
HCM had a myocardial ______ disarray
Fiber
With HCM there’s increased LV hypertorphy and _______load. This causes _____issues and results in _____ dysfunction which results in _____ enlargement.
Afterload; filling; diastolic; LAE
Why does HCM result in LAE?
Because the LV is hypertrophied, unable to relax and fill and is noncompliant. This results in the LA enlarging and LA not filling properly
Due to HCM causing LAE, this can also result in ____
MR
Which is the most common?
A) HOCM
B)HCM
C)SAM
D) ASH
D
IHSSS has what 2 things?
SAM & ASH
HOCM has what 2 things ?
SAM & HCM
With HOCM it has the thickened ___ which causes the AMVL to ?
Septum ; to hit the septum causing an obstruction
MV thickening and scarring may result from?
The MV leaflets constantly striking the thick IVS and obstruction
_____ and fibrosis may be present with HCM
MAC
What are some symptoms of HCM?
-syncope
-sudden death
-arrhythmias
-angina
-DOE
Valsalva or amyl nitrate will ___ the murmur/sound of HCM
Increase
What’s the murmur associated with HCM?
Crescendo descendo -systolic murmur
What are the 4 variants of HCM?
-Sigmoidal
-Reverse curve
-Apical
-Neutral
Which HCM variation is the most common?
A)Apical
B)Neutral
C)Sigmoid
D)Revers curve
C
Describe the Sigmoid HCM variant
The septum is thicker- caused AMVL to hit it
Describe reverse Curve HCM variant
Entire IVS curves downward into LV
Describe apical HCM variant
Apex is thicker than the rest of the walls
Describe Neutral HCM variant
Concentric LVH
How common is the sigmoid HCM variant?
40-50% most common!
How common is the Reverse curve HCM?
30-40%
How common is the apical and neutral HCM?
10%
Apical HCM is more common what country?
Japan
What is the etiology of apical HOCM?
Genetic
With apical HCM on Doppler you will typically see flow ____in mid ____
Acceleration ; LV
With apical HCM you will see increased ___ voltage on EKG. And giant negative ___ wave
QRS; T
The “ace is spades sign” is?
Apical HCM
With HCM the myocardium may a ___ appearance from the ____ disarray
Bright; fiber
With HCM will you have a small LV cavity or thick LV cavity
Small
Pt. With HCM usually have ____ LV contraction or _____ LV contraction
Hyperdyanmic ; normal
Thickness of ventricular walls with HCM may be ____ or ____
Asymmetric or symmetric
If the HCM is asymmetric what is the septal to PW ratio?
A) >1.3-2
B)<1.3-1
C)>1.3 to 1
D)<1.2-2
C) >1.3-1
Duration of septal contact with the AMVL will increase with ___ or ____ of the pt. Is NOT on beta blockers
Valsalva or amyl nitrate
If the pt. Is on beta blockers will valsalva or amyl nitrate increase the septal contact sound?
No
With HOCM there will a _____ closure of Av
Mid systolic
If HCM is obstructive what occurs to the AV?
Mid systolic closure of AV due to obstruction shutting the AV early
LVOT obstruction causes the AV to?
A) flutter in systole
B)close mid systole
C)flutter in systole
D)close late systole
B
Another name for SAM is?
IHSS
HCM will show what kind of MV diastolic dysfunction filling pattern?
A) Restrictive
B) Pseudo normal
C)Abnormal relaxation
D) none of the above
C
The IVRT will be right before the?
E wave
What is the Doppler spectrum of a HCM look like?
Dagger shaped (late peaking jet)