Know It Pt.6 Flashcards
MVP is ____ movement of one or both MV leaflets into the ____
Systolic ; LA
MVP is sometimes linked to ____ ____ disorders such as ________ and may be progressive
Connective tissue; Marfans syndrome
MVP is more common in young ___
Women (5-10%)
The congenital connective tissue disease that causes aortic dilation and Mitral valve prolapse is called?
Marfans syndrome
In Marfans syndrome why does aortic dissections and MVP occur?
A) increased systolic BP
B) aortic arteritis
C) lack of fibrilin
D) lack of collagen
C
MVP can also be caused by ______ ______
Myxomatous Degeneration
___% of people that have MVP will have ____
23% ; Tricuspid valve prolapse
What 5 diseases is MVP associated with?
Marfans syndrome
Secundum ASD
WPW
Lupus
Ehelers-Danlos
What is WPW?
Wolf Parkinson white syndrome is a congenital heart disorder. It’s a syndrome where people have extra pathways for electrical signals to travel between the heart.
This causes a fast heart beat of over 100
What is Lupus ?
Lupus is a autoimmune disorder that causes chronic inflammation by attacking your bodies own tissues and organs and body systems
What is Ehlers-Danlos?
Ehlers-Danlos syndrome is a group of inherited disorders that affect your connective tissues — primarily your skin, joints and blood vessel walls.
What is vascular Ehlers-Danlos ?
A syndrome that can cause the walls of your blood vessels, intestines or uterus to rupture.
What does Gracile Habitus means?
Thin for their tall height
What are some symptoms /signs of people that have Marfans syndrome?
-Garcia’s habitus (thin for their height)
- joint hyper flexibility
- optic lens dislocation
-high arched palate
With pt. That have Eheler Danlos what things should look for on the echo?
MVP
Ao dissection
So dilation
Severe Aortjc aneurysms are greater than?
A) 4.0cm
B) 4.5cm
C)5.0cm
D)7.0cm
C
What are the 2 standards for classifying dissections?
DeBakey scale
Stanford scale
The Stanford scale for aortic dissections has what classifications? Describe then
TYPE A - involves proximal aorta to left subclavian
TYPE B - involves aorta distal to left Subclavian (descending)
The DeBakey scale for aortic dissections has what classifications? Describe then
Type 1- Involves ascending & descending dissections
Type 2- Only involves ascending dissection
Type 3- Only involves descending dissection
A good way to remember the Stanford dissecfion scale va. The DeBakey is that the Stanford scale has ___ & ____ like the grades you want to get at the school!
A’s & B’s
What’s type 2 of the DeBakey scale?
Only ascending dissections
What’s type 3 of the DeBakey scale?
Only the descending dissection
What’s type B of the Stanford scale?
Distal to the left subclavian dissections
___% of people have Type 1 of the Bebakey scale.
60% ; type 1 of DeBakey scale is both ascending & descending
___% of people have Type 3 of the Bebakey scale
30%; Type 3 of the debakey scale is descending dissection only
MVP may cause ___ first which can then cause ______
MR; LAE
Patients with MVP are usually ____
Asymptomatic
What’s the murmur associated with MVP?
Mid systolic murmur / with or without click