HSP article (On Final Only)

Question 1

What two things can help diagnose HSP?

Answer 1

PT history + instrumented gait analysis (cannot always be confirmed by genetic testing)

Pt had full term birth? - HSP

CP is NOT genetic, HSP is

Question 2

What is HSP?

Answer 2

HSP (hereditary spastic paraplegia) is a degeneration of the corticospinal tract and (to a lesser extent) dorsal column fibers characterized by progressive muscle weakness, increased tone, and spasticity of the lower extremities resulting in the predominant clinical feature of gait disturbance

Question 3

What is the critical issue of misdiagnosing someone with HSP as having CP

Answer 3

lack or referral to genetic specialist

those with HSP need to see genetic specialist

Question 4

Is there a difference between HSP and CP in lower body Instrumented gait analysis

Answer 4

no

Question 5

What have they found to be the main difference between HSP and CP in the IGA? (MOST IMPORTANT THING FROM THE ARTICLE PLS MEMORIZE THIS)

Answer 5

Upper body movement:

an atypically large excursion of lateral trunk flexion (typically bilaterally)

cervical translation (cervical retraction/protraction) which is movement of the chin in a forward and backward direction

Note: this is not diagnostic but rather indicates further testing needed if you see these

Question 6

T or F: in the dr.bickleys study the majority of clinicians were confident in the ability to distinguish CP from HSP

Answer 6

F, 95% said no or unsure