Developmental hip dysplasia Flashcards

1
Q

what is developmental dysplasia of the hip?

A
  • A disorder of abnormal development resulting in dysplasia and possible subluxation or dislocation of the hip secondary to capsular laxity and mechanical factors
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2
Q

What does DDH encompass?

A
  • A spectrum of disease that includes
  • DYSPLASIA
  • SUBLUXATION
  • DISLOCATION
  • TERATOLOGIC HIP- identified in utero- has pseudoacrtabulum, assoc with arthrogryposis, myelomeningocele
  • LATE ADOLESCENT
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3
Q

What is the incidence?

A
  • Hip dysplasia 25%
  • scotland 4 per 1000 live births
  • bilateral in 20%
  • most common left hip in females
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4
Q

What are the risk factors?

A
  • First born
  • female 6:1 males
  • breech
  • oligohydraminos
  • FHx
  • assoc with other packaging deformities
    • congential muscular torticolis 20%
    • Metatarsus adductus 10%
    • congenital knee dislocation
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5
Q

What is the pathology meant to be caused by?

A
  • INITAL instability thought to be due to maternal and fetal laxity
  • Genetic laxity
  • Intrauterine and postnatal malpositioning
  • initial laxity-> dysplasia -> gradual dislocation
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6
Q

Where is the normal acetabular deficiency ?

A
  • Anterior or anterolateral
  • In cerebral palsy= posteriosuperior
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7
Q

What is the classification?

A
  • Put into a spectrum of diseases
    • DISLOCATED
      • Ortani positive- reduce hip
    • DISLOCATABLE
      • Barlow positive
    • SUBLUXABLE
      • Barlow positive
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8
Q

How do you diagnose it?

A

Physical exam <3 months

  • ORTOLANI- hip is OUT AND TRY AND REDUCE IT- abduction manoeuvre
  • BARLOW- hip is IN and try push back to dislocate it
  • GALEAZZI- to identify any LLD due to unilate dislocated hip with hip and knees flexed
    • 90 degrees femur short on dislocated hip
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9
Q

In a child older than 3 months what would your clinical findings be in a child with DDH?

A
  • Limited HIP ABDUCTION
    • most sensitive test when contractures start
  • LLD Unequal skin folds- only in unilateral
  • >1 yr when walking
    • pelvic obliquity
    • lumbar lordosis
    • trendlenberg gait- abductor insufficiency
    • toe walking - compensate for shortening of affected side
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10
Q

What age can you use radiographs? why?

A
  • From 4-6 months
  • as this is when the FEMORAL HEAD begins to OSSIFY
  • Tear drop seen at 18 months
    • ​this is quadrilateral space & cotyloid fossa
    • if seen within 6 months of reduction of hip strongly good outcome
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11
Q

What lines on X-ray help you identify hip dislocation in DDH?

A
  • Hilgenreiner’s line= line thru r + l triradiate cartilage
    • Femoral head ossification should N be INFERIOR
  • Perkins line= line perpendicular to hilgenreiner’s thru a point at a LATERAL margin of the ACETABULUM
    • Femoral head ossification should N be medial to this line
  • SHENTON’S line- arc along inferior border of femoral neck and sup margin of obturator foramen
    • arc should be N continuous
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12
Q

What lines on X-ray help you identify hip dysplasia in DDH?

A
  • Acetabular Index- angle formed by a line drawn from point on the lateral triradiate cartilage to point on lateral margin of acetabulum and hilgenreiner’s line
    • should be < 25 degrees in pt>6/12
  • CENTRE EDGE ANGLE of WILBERG
    • angle formed by a vertical line from the centre of the femoral head and a line from the centre of the femoral head to the lateral edge of the acetabulum
    • N is >20 degrees only reliable after 5 yrs
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13
Q

When is USS recommended?

A
  • At 4-6 weeks in baby with
  • risk factors
  • positive physical findings
  • utilized follow Pavlik tx for equivocal exams
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14
Q

What is the use of USS in DDH?

A
  • it is DYNAMIC USS useful before femoral head ossifies at 4-6 months to identify the ALPHA ANGLE
    • Alpha angle created by lines along the bony acetabulum and ilium
    • normal >60degrees
    • BETA ANGLE - angle created by lines along labrum and ilium, normal <55 degrees
    • USED for assessing reduction of hip whilst in PAVLIK HARNESS- avoids unreduced hips eroding acetabulum
    • Not cost effective for routine screening
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15
Q

What is the goal of tx?

A
  • Based on Achieving and Maintaining early concentric REDUCTION in order to prevent FUTURE degenerative joint disease
  • Tx is based on child’s age
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16
Q

When is arthrogram useful in DDH?

A
  • Used to confirm reduction after closed reduction under anesthesia
  • Concentric reduction must be obtained with <5mm of contrast pooling medial to femoral head and the limbus must not be interposed
  • Helps to identify blocks to reduction
    • Inverted Labrum
    • labrum reduces depth of acetabulum by 20-50% adn contributed to growth of acetabular rim
    • older child may be inverted and block cocentric reduction of the hip
    • Inverted limbus- rosethorn sign
    • a pathologic response of acetabulum to abnormal pressure caused by superior migration of the head
    • consists of fibrous tissue
    • Pulvinar
    • ligamentum teres
    • hip capsule constricted by iliopsoas tendon causing hour- glass deformity pf capsule
17
Q

When is Ct useful in DDH?

A
  • Ct study of choice to evaulate reduction after closed reduction and spica casting
  • MRI doesn’t play a significant role in primary diagnosis
18
Q

What is tx birth to 6 months ?

A
  • HIP MUST BE REDUCIBLE
  • Pavlik harness- abduction splinting
  • check at 3 weeks USS to confirm femoral head reduction
  • Requires normal muscle function CI in pt with spina bifidia
  • Outcomes
    • success rate of 90%
    • abandon brace if not successful at 3-4 weeks
19
Q

What happens if no reduction on uss at 3 weeks in a child 0-6 months?

A
  • Discontinue Pavlik harness to prevent pavlik disease
    • Erosion of pelvis superior to acetabulum -> difficulty with closed reduction
    • Consider closed reduction under GA with on table arthrogram as femoral head is not ossified. then spica cast post op MRI to confirm concentric reduction
20
Q

What is tx 6-18 months with a reducible hip ?

A
  • Closed reduction under GA + arthrogram and spica casting
    • arthrogram allows to see femoral head/any obstuctions to reduction
    • Possible adductor tenotomy
    • Spica cast
    • Post op MRI to confirm concentric reduction
21
Q

What happens if this closed reduction fails or 6-18month old unreducable hip? Why does closed reduction fail?

A
  • Then open reduction and spica cast
  • Due to
    • INVERTED limbus
    • Pulvinar
    • HYPERTROPHIED Ligamentum teres
    • ILIOPSOAS CONTRACTURE
    • Capsular constriction
22
Q

What is tx >2 years with residual hip dysplasia ?

A
  • Open reduction and Femoral oseotomy
    • Osteotomy to correct femoral anteversion and coxa valga
    • Also prevent AVN
    • aim is to congruently reduce the femoral head with GROM
    • May add in pelvic osteotomy often > 4yrs and if severe dysplasia accompanied by significant radiographic changes on acetabular side ie. Acetabular index >25 degrees
23
Q

What approach is used to open reduce the hip?

A
  • Anterior- smith peterson
  • As less risk of injury to medial femoral circumflex vessel
24
Q

Could a medial approach be used?

A
  • Yes
  • Advantages can be used in child <12 months
    • directly addresses block to reduction.
    • less blood loss but disadvantages- unable to preform capsulorrhapy and high associated risk of AVN
25
Q

What is the position of the childs hips in the pavlik harness?

A
  • Within safe zone
  • Flexion 90-100 degrees- control anterior straps
  • Abduction 50 degrees- control posterior straps
26
Q

What can positions outwith the safe zone cause?

A
  • Abduction >60
  • Causes
    • **AVN **
      • ​impingment of posteriorsuperior retinacular branch of middle femoral circumflex artery
    • transient femoral n palsy
      • ​due to hyperflexion
27
Q

How long is the harness worn for?

A
  • 23 hours a day for at least 6 weeks
  • uss at 3 weeks to confirm reduced
  • wean out of harness over 6-8 weeks after hip has stabilised
  • confirm hip position with uss every 4-6 weeks
28
Q

What position in the hip placed in the spica cast?

How long do they remain in it?

How frequently are they changed?

A
  • flexion 100 degrees
  • abduction 45 degrees

  • Remain in spica for 3 months
  • Changed every every 6 weeks
29
Q

What pelvic osteotomy would you use in a young child?

A
  • Salter Open triradiate cartilage
  • single osteotomy cut above acetabulum thru ILIUM to sciatic notch acetabulum
  • hinges thru pubic symphysis
  • can provide 20-25 degrees lateral and 10-15 anterior coverage may lengthen up to 1cm
30
Q

What pelvic osteotomy would you use in an older child?

A
  • Triple STEELE
  • Salter osteotomy plus inferior and superior rami cut
  • acetabular reorientation proceedure
  • triradiate cartilage must be open
  • Reorientation proceedure
31
Q

What pelvic osteotomy would you use in a child > 8 years with a closed triradiate cartilage?

A
  • Ganz or A Shelf salvage proeceedure
  • Ganz- multiple ostetomies in the pelvis, ilium and ischium nr the acetbulum- improves 3d correction but technically the most challenging .
  • SHELF- when you add bone to the lateral WB surface of the acetabulum by extra-articular buttress of bone over sublimed femoral head. it depends on the fibrocartilage metaplasia for successful results
32
Q

What the general complications of DDH tx?

A
  • Osteonecrosis
    • All forms of tx
    • excessive/ forceful abduction
    • previous failed closed tx
    • repeat surgery
    • seen on xray- failure of growth of ossificaiton nucleus 1yr after reduction
    • broadening of femoral neck
    • increased density & fragmentation of ossified head
  • Recurrence
    • Approx 10% with appropriate tx
    • radiological follow up until skeletal maturity
  • Delayed diagnosis
33
Q

What if a child presents late with bilateral dislocations if aged 6 or older?

A
  • Pt typically functions better if hips NOT reduced
34
Q

What if a child presents late with unilateral dislocation if aged 8 or older?

What can be done about their LLD?

A
  • Better outcomes without surgical tx if patient aged 8 or more
  • Epiphysiodesis