Congenital Heart Defects Flashcards
What condition is associated with transposition of great vessels?
Maternal diabetes
Cause of transposition of great vessels?
Failure of aorticopulmonary septum to spiral
What determines prognosis in teratology of fallot?
Pulmonary stenosis
CXR findings of teratology of fallot?
Boot shaped - RVH
What do kids with teratology of fallot do to feel better?
Squat - increases afterload and sends more blood to lungs
What congenital heart defect can lithium exposure cause?
Ebstein anomaly
What congenital defect is FAS associated with?
VSD
What determines prognosis in VSD?
FAS
Murmur with VSD?
Holosystolic, harsh murmur
Heart sounds with ASD?
Loud S1
Wide fixed split S2
What defects are most common in ASD?
Ostium secunudum
What is ASD associated with?
Down Syndrome
Murmur with PDA?
machine-like murmur
PDx findings in PDA?
Late cyanosis in lower extremeties (differential cyanosis)
PDA associated with…?
Congenital rubella
Which aortic arch derivative is PDA?
6th
Uncorrected L to R shunts lead to?
Eisenmenger Syndrome
Coarctation of the aorta is associated with…?
Turner Syndrome
PDx of coarcation?
HTN in UE, weak pulses in LE
CXR of coarcation?
Notched ribs
Alcohol exposure in utero
VSD, PDA, ASD, teratology of Fallot
Congenital Rubella
PDA, pulmonary artery stenosis, septal defects
Down Syndrome
AV septal efect (endocardial cushion defect), VSD, ASD
Infant of diabetic mother
Transposition of great vessels
Marfan Syndrome
MVP, thoracic aortic aneurysm, aortic dissection, aortic regurgitation
Prenatal Lithium exposure
Ebstein anomaly
Turner Syndrome
Bicuspid aortic valve, coarctation of aorta
Williams Syndrome
Supravalvular aortic stenosis
DiGeorge Syndrome
Truncus arteriosus, teratology of Fallot