CARDIO Chap 420-445 Flashcards
Mature equivalent of
Bulbus cordis
Right ventricle
Mature equivalent of
Truncus arteriosus
Aorta & pulmonary artery
Mature equivalent of
Sinus venosus
Atria
Radial-Femoral delay (radial pulse felt prior to femoral pulse)
Coarctation of the aorta
Mid systolic click
Mitral valve prolapse
Pulmonary ejection clicks
Pulmonary stenosis
ECG: Positive T wave in V4R and V1, Tall R wave and deep S wave in V6 in an infant
RVH
*Normal infants has inverted T waves in V4R, V1 and V3R until 2 years
Tall (>2.5mm), narrow, spiked P waves
Right Atrial enlargement (PS, Ebstein anomaly, Tricuspid Atresia)
Broad, bifid, biphasic P waves
Left Atrial enlargement (large left to right shunts)
*Remember B
Flat P wave
Hyperkalemia
Mutation in dystrophin gene (chromosome Xp21)
Dilated Cardiomyopathy
MC form of ASD
Ostium secundum defect
7yo, Patient came in due to exercise intolerance
No symptoms prior
Pe: left precordial bulge, palpable right ventricular systolic lift at left sternal border, noted FIXED WIDELY SPLIT 2ND heart sound in ALL PHASES of respiration, and SYSTOLIC EJECTION murmur heard at left middle and upper sternal border
CXR: Enlarged pulmonary artery, increased pulmonary vascularity
Atrial Septal defect
Scimitar syndrome
- cresenteric shadow of vascular density along the right border of cardiac silhouette seen in CXR
Partial Anomalous Pulmonary Venous Return (PAPVR)
Down syndrome with wide fixed splitting of S2 and apical holosystolic murmur that radiates to the left axilla
Atrioventricular Septal defect
MC cardiac malformation
VSD
MC type of VSD
Membranous type
VSD associated with Aortic Regurgitation
More common in Asian & males
Supracristal VSD
Continuous systolic machinery-like murmur best heard at the 2nd left intercostal space that radiates to the left clavicle
Patent Ductus Arteriosus (PDA)
Pulmonary stenosis secondary to valve dysplasia
MC cardiac anomaly in?
Noonan syndrome
MC right ventricular outflow obstruction
Isolated Pulmonary Stenosis
Initial treatment of choice for pulmonary stenosis
Balloon Valvuloplasty
T/F: Clinical manifestations of Acyanotic heart disease with obstructive lesions (VALVULAR STENOSIS) depends on the degree of obstruction
True
Endocardial fibroelastosis (endocardial fibrous scarring associated with which type of obstructive heart lesion)
Aortic Stenosis
Risk of sudden death during or immediately after exercise if unoperated
Severe Aortic Stenosis
MC origin of coarctation of the aorta
Juxtaductal coarctation (below the origin of the left subclavian artery at the origin of the ductus)
Hypertension in upper extremities but low blood pressure in lower extremities
Bounding pulses on the upper extremities with weak pulse lower extremities
CXR: notching of inferior border of the ribs
Coarctation of the aorta
*notching of inferior border of the ribs - due to pressure of collateral vessels
SHONE complex
Mitral stenosis
Subvalvar Aortic Stenosis
Coarctation of the aorta
High-pitched, apical holosystolic murmur
CXR: Left atrial and ventricular enlargement
ECG: Bifid p waves
Mitral insufficiency
*Bifid p waves (LA enlargement)
Late systolic apical murmur preceded by a click
Associated with Marfan syndrome & Ehler-Danlos syndrome
Mitral valve prolapse
-billowing of one or both mitral leaflets especially posterior cusp at the end of systole
Test to distinguish cyanotic congenital heart disease from pulmonary disease
Hyperoxia test
Cyanotic congenital heart disease with primary defect is an anterior deviation of the infundibular septum
Tetralogy of Fallot (TOF)
Complete obstruction of the right outflow tract
Pulmonary atresia
Cyanotic child, hyperpneic and restless, gasping
Pe: dusky skin, clubbing of fingers, with left anterior hemithorax bulge
Diagnosis?
Management?
Paroxysmal hypercyanotic attack (Tet spell) in TOF
Knee to chest position
Morphine (0.2mg/kg)
Propanolol (0.1mg/kg)
If severe, correct acidosis with Sodium bicarbonate
*loud systolic murmur of TOF usually disappears in Tet spells
Boot shaped heart in CXR (coeur en sabot)
Tetralogy of Fallot
TOF is commonly associated with what syndrome
Di George Syndrome (CATCH 22)
Cardiac anomalies Abnormal facies Thymic hypoplasia Cleft palate Hypocalcemia Deletion in chomosome 22q11.2
Medication to maintain patency of ductus arteriosus especially in ductal dependent heart disease
Prostaglandin E1 (0.01-0.2umg/kg/min)
Medication ised to decrease frequency and severity of hypercyanotic spells
Oral Propanolol (0.5-1mg/kg every 6 hours)
Palliative systemic-to-pulmonary artery shunt in TOF
Blalock-Taussig shunt
Cyanosis with left axis deviation and LVH in ECG
Tricuspid Atresia
Downward displacementnof an abnormal tricuspid valve into the right ventricle
Ebstein Anomaly
CXR: Boxed shaped heart
Ebstein anomaly
CXR: Egg on a string
Transposition of Great Arteries (TGA)
Neonate presents with dyspnea & cyanosis in the first hour of life. Unresponsive to hyperoxia test. O2 sat is 75%
(+) Maternal DM
CXR: Egg on a string
Transposition of Great Arteries
Treatment of choice for d-TGA
Arterial switch (Jatene) procedure
T/F: Obstructive TAPVR is a pediatric cardiac emergrny
True. Because prostaglandin is ineffective
T/F: Obstructive TAPVR is a pediatric cardiac emergrny
True. Because prostaglandin is ineffective
CXR: Snowman sign or Figure of 8
*perihilar pattern of pulmonary edema
Total Anomalous Pulmonary Venous Return
Single arterial trunk arises from the heart
VSD always present
Truncus Arteriosus
Pulmonary vascular obstructive disease and right-sided heart failure
Pulmonary Hypertension