Biliary Pathology Flashcards
What is a choledochal cyst?
a congenital, focal, or diffuse cystic dilation of the biliary tree
what are the risk factors of a choledochal cyst?
- more common in men
- increased incidents in infants
- associated with gallstones, pancreatitis, and cirrhosis
what are the symptoms of a choledochal cyst?
- abdominal mass
- pain
- fever
- jaundice
sonographic appearance of a choledochal cyst
appear as cysts in an ultrasound
- anechoic
- echogenic walls
- posterior enhancement
- round
define Caroli’s Disease
a rare congenital abnormality most likely inherited in an autosomal recessive fashion.
what is Caroli’s Disease associated with?
characterized by congenital segmental saccular cystic dilation of major intrahepatic bile ducts
- usually found in young adults or pediatric patients
- renal disease
- congenital hepatic fibrosis
symptoms of Caroli’s Disease
- recurrent cramplike upper abd pain
- secondary to biliary stasis
- ductal stones
- cholangitis
- hepatic fibrosis
- cystic disease of the kidneys (ADPKD)
what is considered a dilated duct?
where the CHD has an internal diameter of greater than 4mm
what is the most common cause of ductal dilation?
the presence of an obstruction like a tumor or thrombus within the ductal system
how does ductal dilation appear on US?
it appears as the “shotgun” symbol on US when the intrahepatic ducts are dilated
what can cause on obstruction of the distal CBD?
the most common cause is pancreatic carcinoma, choledocholithiasis, and chronic pancreatitis with stricture formation
define cholangiocarcinoma
a rare malignancy that originates in the CBD or CHD.
where is cholangiocarcinoma usually located?
in the CBD or CHD
what is a specific type of cholangiocarcinoma that occurs in the CHD?
a Klatskin’s tumor is a specific type of cancer that occurs in the CHD.
appearance of a Klatskin’s tumor
although the mass may not show up on ultrasound, a nonunion of the right and left hepatic ducts is a characteristic of a Klatskin’s tumor
define Mirizzi syndrome
Mirizzi syndrome is an uncommon cause for extrahepatic biliary obstruction as a result of an impacted stone in the cystic duct
what are the symptoms of Mirizzi syndrome?
painful jaundice