ALS

Question 1

What is ALS

Answer 1

Relentlessly progressive an incurable neurodegenerative Disorder that causes weakness disability and death

Question 2

Survival rate

Answer 2

Usually 3 to 5 years. 10% can live 10 years or more

Question 3

Clinical manifestations

Answer 3

Asymmetric limb weakness is the most common, fatigue, dysarthria, dysphagia, muscle atrophy in spaces Citi, twitching of face or tongue, respiratory muscle weakness which is life-threatening

Question 4

Are these patients still cognitively intact as the condition worsens

Answer 4

Yes

Question 5

Riluzole

Answer 5

Only FDA approved medication for ALS, not a cure but extend survival time

Question 6

Plan of care

Answer 6

Moderate Lee intense endurance type exercises for trunk and limbs, support cognitive and emotional functions, facilitate communication, speech therapy as needed, maintain NPO if major risk for aspiration, pain assessment, minimize risk of injury, provide diversional activities, facility patient and family anticipatory craving