5-23

Question 1

Rx for acetaminophen ingestion

Answer 1

N-acetylcysteine

Question 2

Jones criteria

Answer 2

Joints 
<3 (carditis) 
Nodules 
Erythema marginatum 
Sydenham chorea

Question 3

ASD heart sounds

Answer 3

Fixed split second heart sound

Question 4

12 yo w/ recurrent episodes of facial swelling; fam hx of similar episodes

Answer 4

hereditary angioedema; mut C1 esterase inhibitor

Question 5

risk of cardiac defect in future sibling of child w/ one

Answer 5

2-6% (1% in gen pop)

Question 6

asymptomatic child w/ fixed split S2 + RV systolic lift at L sternal border

Answer 6

ASD

Question 7

child w/ fever, polymorphous rash, hand/feet swelling, conjunctivitis

Answer 7

kawasaki dz

Question 8

1st line tx for infant w/ SVT

Answer 8

carotid massage (immersion of face in cold water, etc) -> adenosine if that doesn’t work

Question 9

infant w/ heart failure, tricuspid regurg, mid-diastolic murmur @ L lower sternal border, RV conduction block

Answer 9

ebstein anomaly (downward displacement of tricuspid valve)

Question 10

child w/ nml echo, no cyanosis, w/ brief episode of SVT during activity

Answer 10

WPW

Question 11

child w/ episodes of high spiking fever, rash over chest/back, upper sternal pain, swollen fingers, hepatosplenomegaly, pericardial effusion

Answer 11

JIA

Question 12

tricuspid atresia causes __VH and __ axis deviation

Answer 12

Left - b/c hypoplastic R heart

Question 13

cyanosis in 6hr old infant w/ nml sized heart, nml pulm vasc markings, RVH + RAD

Answer 13

transposition of great vessels

Question 14

adolescent w/ late apical systolic murmur preceded by a click; nml ECG + CXR

Answer 14

mitral valve prolapse

Question 15

how to open vs close a PDA

Answer 15

open = PGE1, close = indomethacin

Question 16

male w/ turner syndrome-like features; associated cardiac abnormality?

Answer 16

Noonan, pulmonic stenosis

Question 17

adolescent w/ new onset syncopal episodes (cardiac abnormality)

Answer 17

long QT

Question 18

neonate w/ thrombocytopenia, neutropenia, rash, liver abnormalities, congenital heart block

Answer 18

neonatal lupus (from mom’s SLE IgG antibodies)