[3] Abnormalities of Development of the Reproductive Tract II

Question 1

Describe: Meyers-Rokitansky Syndrome

Answer 1

Absence of a vagina combined with abnormal/absent uterus

Question 2

What is Chordee

Answer 2

Ventral Curvature of the Penis

Question 3

What causes Chordee of the Penis

Answer 3

Failure of the spongiosum to develop

Question 4

Modality of choice to diagnose reproductive tract anomalies

Answer 4

MRI

Question 5

Cloacal formation is caused by the non-development of?

Answer 5

Urorectal Septum

Question 6

Cause of Proximal Vagina Atresia

Answer 6

Failure of Mullerian Ducts to fuse to form Mullerian Tubercle

Question 7

Cause of Distal Vaginal Atresia

Answer 7

Failure of proliferation of Sinovaginal Bulbs from the Urogenital Sinus

Question 8

Presentation of Vaginal Atresia in Infancy

Answer 8

Hydrocolpos

Question 9

What is Uterus Didelphys

Answer 9

Complete bicornuate uterus with two cervices caused by non-fusion of paramesonephric ducts

Question 10

Cause of Unicornuate Uterus

Answer 10

Aplasia of one paramesonephric duct

Question 11

This penile abnormality is very common in fat individuals

Answer 11

Hidden Penis

Question 12

Cause of Congenital Absence of Scrotal Sacs

Answer 12

Non-fusion of the Labio-Scrotal Swellings

Question 13

Definition of a True Undescended Testis

Answer 13

Testis is undescended but still along the normal pathway

Question 14

Hernias present more commonly on which testis? Why?

Answer 14

RIght, because the processus vaginalis closes later on this side

Question 15

What type of infants have a higher risk for testicular maldescent?

Answer 15

Premature Infants

Question 16

If no testis develops before 8 weeks AOG what genitalia forms?

Answer 16

Female Genitalia

Question 17

If the testis does not develop from 8-10 weeks AOG what genitalia forms?

Answer 17

Ambiguous Genitalia

Question 18

If the testis does not develop after the 14 week AOG what genitalia forms?

Answer 18

Normal Male Genitalia (Vanishing Testis Syndrome)