Pulmonary Stenosis

Question 1

What is congenital pulmonary valve stenosis

Answer 1

usually valve conists of 3 leaflets, some can develop abnormally, becoming thickened or fused. This causes narrow opening between right ventricle and pulmonary artery

Question 2

Diagnosis of pulmonary valve stenosis

Answer 2

Often asymptomatic so discovered on routine baby checks incidentally

Question 3

Symptoms of pulmonary valve stenosis

Answer 3

More severe forms can present with fatigue, SOB, dizziness, fainting, palpable thrill, ejection systolic murmur, RV heave, raised JVP with giant A waves

Question 4

Murmur in pulmonary valve stenosis

Answer 4

Ejection systolic murmur, loudest over pulmonary area

Question 5

Management of congenital pulmonary valve stenosis

Answer 5

ECHO, watch and wait, balloon valvoplasty via venous catheter is treatment of choice if valve is significantly stenosed

Question 6

What condition is associated with pulmonary stenosis

Answer 6

Noonan syndrome