Prion Disease Flashcards
1
Q
Kuru
A
Progressive neurodegenerative disease
Transmitted via cannibalism
2
Q
Sporadic familial and iatrogenic Creutzfeldt-Jakob Disease
A
Rapidly progressive neurodegenerative disorder characterized by myoclonus, behavior changes and dementia
**Most common human prion disease
3
Q
New variant Creutzfeldt-Jakob disease
A
Associated with bovine spongiform encephalopathy (BSE)- “mad cow disease”
4
Q
Fatal familial insomnia
A
Inherited prion disorder that has as its hallmark a progressive course of insomnia that worsens over time until the patient barely sleeps or does not sleep at all.
Autonomic instability that usually manifests as what appears to be increased sympathetic tone.
