Pediatrics: Special Forms of Strabismus Flashcards
Goldenhar syndrome, Wildervanck syndrome
two syndromes associated with Duane syndrome
retraction on adduction, restricted horizontal eye movement, vertical shoots
three essential features of Duane syndrome
AD
though usually sporadic, 5-10% of cases of Duane syndrome are inherited in this manner
absence of the CN VI nucleus
MRI finding in Duane syndrome
type I
Duane syndrome with esotropia in primary gaze and primary abduction defect
type II
Duane syndrome with exotropia in primary gaze and primary adduction defect
type III
Duane syndrome with small heterotropia (or none) and marked limitation of both adduction and abduction
resection
type of surgery that is recommended against in Duane syndrome
deviation in primary position, head turn, large shoots, marked globe retraction
four indications for surgery in Duane syndrome
MR recession
typical surgery for type I Duane’s syndrome
LR recession
typical surgery for type II Duane’s syndrome
none
typical surgery for type III Duane’s syndrome
spontaneous resolution
Prominent feature of acquired Brown syndrome that is less common (though not entirely unusual) in congenital Brown syndrome
globe retropulsion
what maneuver will worsen restriction in Brown syndrome, in contrast to IR restriction?
primary gaze hypotropia, downshoot in adduction
two additional findings in severe Brown syndrome
intermuscular septum
In superior oblique tenotomy with spacer, care must be taken to repair this to prevent downgaze restriction
50%
percentage of cases of CN III palsy in children that are congenital
aberrant regeneration, miosis
two prominent features of congenital CN III palsy that help distinguish it from acquired