Ma'am Oledan 2 semis Flashcards
congenital aganglionic megacolon
Hirschsprung disease
characterized by persistent constipation: partial or complete intestinal obstruction
Hirschsprung Disease
congenital anomaly thatt results in mechanical obstruction
Hirschsprung Disease
absence of ganglion cells results in loss of rectosphinteric reflex
results in a lack of enteric nervous system
HD internal sphincter does not relax
Hirschsprung Disease
a midline defects of the spinal cord
involving the failure of the osseous
(bony) spine to close
- common defects of CNS
Spina Bifida
two categories of Spina Bifida
- SB occulta
- SB cystica
refers to a defect that is not visible
externally It occurs most commonly
in the lumbosacral area
- Spina Bifida Occulta
it is not apparent unless there is
neuromuscular disturbances (static
changes in gait, foot deformity,
bowel and bladder disturbance)
. Spina Bifida Occulta
- skin depression or dimple
- port-wine angiomatous nevi
- dark tufts of hair
- soft subcutaneous lipomas
- Spina Bifida Cutaneous indications
refers to the visible defects with an
external saclike protrusion
. Spina Bifida Cystica
Two major forms SB Cystica
Meningocele
Myelomeningocele
which encases
meninges and spinal fluid but no
neural elements
Meningocele
which contains
meninges, spinal fluid and nerves
Myelomeningocele
(meningomyelocele)
related to to the normal formative
stages of the nervous system on the
first trimester of pregnancy
Spina bifida causes
it requires a multidisciplinary
approach involving the specialties of
Neurology,
Neurosurgery, Pediatrics, Urology,
Orthopedics, Rehabilitation, Physical
Therapy, Social Service and
intensive nursing care in a variety of
specialtyareas
Management of spINA BIFIDA
s a syndrome or sign resulting from the
disturbances in the dynamics of CSF
Hydrocephalus
Hydrocephalus caused by various conditions such
as:
- Congenital
- Acquired condition (intraventricular
hemorrhage, tumor, CSF infection,
or head injury)
Three Factors that Influence the dinical
picture in hydrocephalus are the following:
- Acuity of onset
- Timing of onset
- Associated structural malformation.
predominant sign in hydrocephalus infant
head enlargement
in older infants
and children the lesions responsible for
hydrocephalus produce
adjacent structures
other neurologic signs through pressure on
Preterm infant with hydrocephalus is high
risk for
Intraventricular hemorrhage
Signs of Hydrocephalus in Infant
-Head grows in an abnormal rate
-Bulging of fontanels (with or without head
enlargement)
-Anterior fontanel is tense
-Scalp veins are dilated esp. when the baby
cries
Signs of Hydrocephalus in Children
-Check the ICP (Intracranial Pressure) if it is
increased.
-If ICP increased the child will complain
headache on awakening with improvement
later
-Followed by emesis, uprate posture,
strabismus
-Irritable, lethargic, confuse and incoherent
PERINAUD SYSNDROME
UPGAZE PALSY