Lung Diseases: Cystic Fibrosis

Question 1

cause of CF

Answer 1

genetic mutation, affects sodium chloride channels

Question 2

CF

Answer 2

systemic, progressive lung disease that can lead to respiratory failure

• expression of genetic mutation varies
• multisystem effect

Question 3

epidemiology

Answer 3

• most common inherited disease in Caucasians

- equal gender distribution

Question 4

effect on breathing

Answer 4

• thick sticky mucus, hard to move, clogs nasal passages and sinuses
• bacteria gets trapped, causing infections and lung damage

Question 5

lung sounds

Answer 5

• crackles
• rhonci
• wheezes
• decreased lung sounds

Question 6

mediate percussion lung sounds are ____

Answer 6

hyper-resonant

Question 7

patient’s with CF are often recipients of lung/heart transplants. what is needed after this?

Answer 7

cardiopulm PT needed after transplant

Question 8

PT treatment includes

Answer 8

airway clearance, active cycle of breathing, percussion, vibration, PEEP device, autogenic drainage, exericse, high frequency chest wall oscillation

Question 9

prognosis

Answer 9

can lead a normal life w/o severe disability with meds, but complications worsen with age
- avg lifespan is 37. usually die of lung complications