Limb Deficiencies Flashcards
Rate of phantom pain/sensation in congenital limb-deficient children
Zero
What is the preferred classification system for pediatric limb deficiencies
ISPO (international Society for Prosthetics and Orthotics)
Most common congenital lower limb deficiency
Fibular longitudinal deficiency
What is Holt-Oram Syndrome
Limb deficiencies associated with CHD
Most common complication seen after amputation in an immature child
Terminal overgrowth
Absence of a limb
Amelia
Partial absence of a limb
Meromelia
procedure for PFFD that rotates foot by 180 degrees and attached to shortened femur, allowing ankle to control prosthesis
Van Ness Rotation
Treatment of choice for a transtibial deficiency
Knee disarticulation
When is a more sophisticated transradial prosthesis and terminal device fitted for a child after the initial prosthesis?
11-13 months when child can walk
What kind of procedure is usually done for severe forms of PFFD
Fusing shortened femur to tibia and doing a Syme’s amputation
When does first prosthetic fitting for a transradial deficiency occur for a child?
6-7 months, when they can first sit
MC prosthetic foot used for a child amputee
SACH foot
Procedure used to separate ulna and radius in forearm to create prehensile surface
Krukenberg procedure
What is VACTERL syndrome
Vertebral defects Anal atresia Congenital defect TracheoEsophageal fistula Renal dysplasia Limb deficiency
Missing hand or foot
Acheiria
At what age can a child operate all types of prosthetic components for a transradial deficiency?
4-5 years
Absence of half a limb
Hemimelia
MCC of pediatric acquired amputation
Trauma
What kind of amputation is preferred in pediatrics to preserve the epiphyseal growth place
Joint disarticulation
What procedure is done if there is fibular deficiency and severe leg length discrepancy
Syme’s amputation
How often should prosthesis be replaced in a growing child?
<5yo = q12 mths 5-12yo = q18 mths 12-21yo = q24 mths
According to ISPO, what does transverse vs longitudinal mean?
Transverse = no distal remaining portions Longitudinal = distal portions remain intact
Absent finger or toe
Aphalangia
Absent metacarpal or metatarsal
Adactyly
Which trimester are congenital limb deficiencies formed?
First trimester
Most common congenital limb deficiency
Left terminal transradial deficiency
At what age can you use body-powered hooks for transhumeral deficiency
2-3 years
What is Fanconi’s syndrome
Limb deficiencies associated with Anemia and leukopenia
What is TAR syndrome?
Thrombocytopenia with
Absence of
Radius
70-80% of patients with PFFD also present with deficiency of………
Fibula
Treatment of choice for terminal overgrowth
Surgical revision
What bones does terminal growth MC occur in, in descending order
Humerus, fibular, tibia, femur
At what age can children use motorized wheelchairs
5-6 years
Longitudinal deficiency of the femur
Partial proximal femoral focal deficiency (PFFD)
Flipper-like appendage attached to trunk
Phocomelia
At what age is prosthetic fitting done for a LE amputee
9-10 months, when child can pull to stand
Most frequent tumors that causes pediatric acquired amputation
Osteosarcoma and Ewing’s sarcoma
