Lecture 2.2 Flashcards

1
Q

How was hearing loss identified in the early days of audiology?

A

100 dB signal played directly into the babies ear at the newborn phase

determines if the baby responded at all to see if they can hear
- only really ruling out profound deafness - signal is so loud

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
2
Q

What recommendations emerged from 1967 National Conference on Education of the Deaf?

A

children with higher likelihood of developing hearing loss are tested
- high risk register to facilitate identification

testing of infants and children 5-12 months should be investigated

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
3
Q

What did White 2010 studies show about screening based on high risk register?

A

if you only screen children with a risk factor, only going to catch 50% of children

other 50% don’t have a risk factor

need to screen early and universally

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
4
Q

How has the view on deafness changed over the years?

A

16th century - recognized deafness was a barrier to communication not an intellectual deficit

late 19th century - deafness viewed as a problem belonging to the field of education

1960s - acknowledge significant delays if hearing loss not identified early
- screened high risk infants first

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
5
Q

What is JCIH?

A

joint committee on infant hearing

formed in early 1970s

addresses populations to be screened, methods and protocols to be used for screening, and later guidelines for early ID and intervention

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
6
Q

What are soundfield systems? How were they used?

A

speaker systems set up in classroom, connected to microphone for speaker

early versions used in educational settings

later determined children with hearing loss benefit from sound access throughout the day
- children later able to wear binaural hearing aids on the body using a harness

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
7
Q

What developments in prescriptive formulae occurred in the 1980s?

A

appropriate hearing aid gain, output, and frequency response was studied extensively

prove mic systems became available

CIs approved for use with children

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
8
Q

What is gain?

A

prescribed amount of volume provided by hearing aid based on hearing thresholds and ear canal volume

we adjust to meet targets

in dB SPL

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
9
Q

What is the goal of rehabilitative and educational management of children with hearing loss?

A

overcome or minimize the barriers to communication imposed by hearing loss in order to enable learning and participation to society

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
10
Q

What 2 categories did children with hearing loss historically fall into?

A

those who had considerable access to acoustic speech signals

those who had limited or no access to speech despite the best technology

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
11
Q

What 2 parallel rehabilitaiton and educational management philosophies evolved?

A

manual approach - visual-based system, natural for those who are deaf (those who can’t or chose not to access speech through technology)

oral approach - spoken communication

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
12
Q

What was the average age of hearing loss identification before the infant hearing program? What are the impacts of this?

A

2.5 years

late identification = window to access/learn speech, language, and literacy closes, impairs social and cognitive development

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
13
Q

What factors result in good language outcomes?

A

good hearing aid fittings
consistent hearing aid uses
language input (quality and quantity)

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
14
Q

What is UNHS?

A

population screening of all babies, regardless of the presence/absence of risk, for the possibility of hearing loss

component of EHDI programs

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
15
Q

What are EHDI programs?

A

Early hearing detection and intervention

comprehensive public health program including UNHS, audiology assessment, hearing loss management, family support, language development support, and monitoring of infants and outcomes

go beyond population screening and offer services to confirm presence of hearing loss and provide intervention services

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
16
Q

What is the importance of early detection and intervention?

A

saves society money on more intense remediation

supports language development, child development, psychosocial well-being, behaviour, and academic success

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
17
Q

What is the prevalence of children born with hearing loss?

A

1-3 / 1000 births

progressive and late onset losses underestimated

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
18
Q

What is screening?

A

a strategy used to identify the possible presence of a yet undiagnosed condition in a population without signs or symptoms

not diagnostic or therapeutic - no resources for follow up

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
19
Q

What is assessment?

A

evaluation of health status to detect disease or condition

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
20
Q

What is intervention?

A

the act of intervening with the intent of modifying outcome

technology and/or language services

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
21
Q

What is the definition of deaf?

A

condition where a person has little or no hearing in both ears

also used to describe a person with this condition whose preferred mode of communication is spoken language

the audiological term - but usually profound bilateral hearing loss used

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
22
Q

What is the definition of Deaf?

A

members of a sociolinguistic and cultural group whose preferred method of communication is sign language

involvement in Deaf community is distinctive feature
- don’t need to have hearing loss (ex. spouse who uses signs to partner)

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
23
Q

What is the definition of hard of hearing?

A

permanent partial or total inability to hear in one or both ears

this term is used to describe a person who has the condition and whose usual method of communication is spoken language

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
24
Q

What is the definition of permanent hearing loss?

A

hearing loss of a particular degree (target level) in any ear caused by disorders of the cochlea, brainstem auditory pathways, or structural abnormalities affecting sound conduction through the external or middle ear structures

hearing loss is permanent if it will not resolve spontaneously and will present a loss of hearing sensitivity in the absence of intervention

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
25
Q

What is the importance of EHDI programs?

A

critical in lives of Deaf/deaf or hard of hearing children to ensure optimized language, literacy, and social skill development

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
26
Q

What are the 5 components of EHDI programs?

A

universal screening

identification of babies with permanent hearing loss
- using evidence based diagnostic techniques

provision of evidence-based intervention services
- including support for technology and communication development

provision of family support

monitoring and measuring
- impact of interventions and program

27
Q

What are the updated EDHI recommendations?

A

1-3-6 rule

all infants should undergo hearing screening by 1 month

all infants who fail screening will have a complete audiological assessment by 3 months

early intervention services should begin as soon as possible after diagnosis, no later than 6 months

regions that meet 1-3-6 should strive for 1-2-3

28
Q

What did the CIHTF report card on EDHI programs find?

A

BC = excellent (only province)
Ontario = good

Canada overall grade = insufficient
- some of EHDI components missing or not implemented in certain provinces

29
Q

What is the Ontario IHP?

A

infant hearing program

identifies children born Dd/HH through UNHS or audiological assessment

provides support and services for children birth-grade 1 who are identified with permanent hearing loss and their families

30
Q

What is the target population of the IHP?

A

infants with permanent hearing loss
- sensorineural greater than 25 dB HL
- auditory neuropathy spectrum disorder
- conductive losses lasting 6+ months

children under 6 with PHL
- have to pay to see audiologist in the community after age 6

31
Q

What populations are NOT targeted by IHP?

A

children of any age transient hearing disorders due to middle ear fluid and/or infection
- such disorders (when cochlea functioning normally) are the domain of OHIP or fee for service audiology clinics

NOT an alternate system for audiometric services in active medical/surgical management of conductive hearing disorders

32
Q

What are the outcomes of the IHP?

A

in each year since implementation, IHP has screened 95-97% of Ontario babies
- exceeds 90% target

each year screens over 132,000 infants and identifies ~450 infants with PHL
- over 2 million newborns screened since its creation

33
Q

What are the components of the Ontario IHP?

A

UNHS
- for Ontario-resident infants 2 months of age of younger

audiological surveillance
- for all infants with risk indicator known to cause late onset/progressive PHL

hearing assessment
- to confirm presence of PHL and provide referrals

intervention/support
- for infant/family if PHL confirmed

evaluation of need for assistive technology

34
Q

Who are the service providers within the IHP?

A

all are trained in IHP protocols/have experience with patients with PHL

UNHS often provided by nurses or CDAs

audiologists provide assessment and amplification services

social workers provide family support

SLPs or ASL consultants provide language development services

35
Q

How is the IHP delivered?

A

regional lead agencies across the province deliver the program in accordance to guidelines
- deliver some or all IHP services in local areas

lead agencies include hospitals, public health units, Children’s treatment centres

complex, comprehensive service delivery pathway

36
Q

What components are in place to ensure consistency of EHDI components in Ontario?

A

evidence-based, mandatory protocols
uniform equipment
mandatory standardized training for service providers
outcome measurement

37
Q

What is the UNHS protocol?

A

complex, comprehensive series of steps based on results of screening

all benchmarks to be completed by 1 year

38
Q

What is the IHP hearing screener’s role?

A

explain screening
obtain consent/documentation
assess for risk factors
conduct hearing screening
explain results
provide next steps

39
Q

What is a risk indicator?

A

identifiable characteristic of a child or medical procedure that is associated with increased likelihood of PHL in the child

identified by IHP screener through document review, consulting medical staff, and talking to family

40
Q

What is the purpose of the risk fator assessment?

A

determine whether screening should be bypassed

decide what type of screening test to use

record information that will determine whether infant should receive later testing (surveillance) and if so what type of surveillance

41
Q

How are risk factors grouped?

A

into 3 categories that determine next steps

no surveillance, surveillance, intensive surveillance/further referral

42
Q

What test is used for the UNHS?

A

ADPOAE (automated distortion product otoacoustic emission) and/or AABR (automated auditory brainstem response)

identifies need for further hearing assessment by IHP audiologist

43
Q

What infants are identified as being at risk?

A

those with one of the pre-defined risk factors for PHL

these babies will instead be screened using AABR (PHL risk is already 10x higher and ADPOAE will not detect specific risk factors)

44
Q

How are at risk babies grouped?

A

at risk babies (group 1 and 2 risk factors) will be screened using AABR

babies with group 3 risk factors will bypass screening and go directly to audiological assessment

group 1 - AABR screen, discharge if pass
group 2 - AABR screen, surveillance if pass
group 3 - do not screen, directly to audiology

45
Q

What are group 3 risk factors that would cause babies to bypass screening and go directly to audiology assessment?

A

atresia/microtia
meningitis
cCMV
positive genetic screen

46
Q

Why is the way the hearing screener communicates with families important?

A

accurate and consistent info helps establish families’ trust in IHP services

sets stage for family’s first impression of IHP program, effectiveness of program, confidence in abilities of screener, willingness to follow recommendations

47
Q

What are standardized scripts?

A

used by hearing screeners in Ontario

standardize the way information is provided throughout the program

reduce family anxiety, facilitate families proceeding with follow-up, supports delivery of high quality information

48
Q

What are possible next steps after screening?

A

discharge
community screen
audiology high risk surveillance
audiology assessment

49
Q

What is the dried blood spot screening?

A

IHP in collaboration with newborn screening Ontario (NSO) determined it was possible to detect certain causes of PHL that might not otherwise be identified through dried blood spot screening

infant heel prick

targeted conditions chosen due to prevalence and ability to be detected by existing blood spot screening

only one in the world!

improves effectiveness of risk assessment process, allow for earlier and more accurate identification of risk factors

50
Q

What is cCMV?

A

herpes family virus causing mild or asymptomatic infection in healthy individuals

potential for serious infection in fetuses or immunocompromised hosts

leading cause of non-genetic sensorineural hearing loss

second leading cause of intellectual disability after Down syndrome

51
Q

What is the positive predictive value of cCMV bloodspot screen?

A

very high - >98% - reported as “detected’

with high viral load of cCMV, babies’ risk of developing hearing loss is 1/3 if symptomatic and 1/10 if asymptomatic

52
Q

What is the positive predictive value of genetic mutation?

A

very high - >98%
nearly assured to have it if screened possible

53
Q

What is positive predictive value?

A

how likely is it the baby really has that condition when test comes back positive

54
Q

What is negative predictive value?

A

if the test is negative, how likely it is that the baby really does not have that condition

55
Q

What is the negative predictive value of genetic mutation?

A

very high

if screen negative, very unlikely to have these mutations

56
Q

What is the care pathway if screened cCMV positive?

A

retrieval managed by NP

refer to community paediatrician for initial evaluation

infectious disease referral for symptomatic infants

referral for ABR assessment ASAP

57
Q

What is the care pathway if genetic screen is positive?

A

retrieval managed by genetic counsellor/audiology team

ABR assessment by audiology

refer to ENT and genetics

58
Q

What is audiological surveillance?

A

proactive recall for audiological appointment of children at risk of developing late onset or progressive hearing loss

symptomatic process for early detection of PHL not detected by UNHS

basic = single point
intensive = multi-point

59
Q

What is the purpose of audiological assessment?

A

determine presence of PHL

estimate hearing levels in each ear at several frequencies

determine type and configuration of PHL for prompt and accurate hearing aid fitting

60
Q

How is audiological evaluation completed between 0-6 months?

A

estimates of hearing sensitivity derived from ABR measurements

hearing aid selection and fitting done using ABR threshold estimates

done in sleeping babies

61
Q

What is the role of the family support worker?

A

share information with audiologist

help with financial applications

support chosen language development pathway

facilitate parent-to-parent connections

62
Q

How does language development begin in infants with PHL?

A

families supported in choosing a language development path
- sign (ASL consultant) or spoken (SLP)

aim for services to start no later than 6 months, as close to home as possible

63
Q

What are the 3 main factors influencing outcomes in children with hearing loss?

A

consistent hearing aid use
- at least 10 hours/day

audibility
- how well sound is heard
- controlled by audiologist

linguistic input
- quality and quantity