heart disease in diff systemic conditions [mostly rare]

Question 1

acromegaly

Answer 1

high bp

LVH

hypertrophich cardiomyopathy

high output Cardiac failure

CAD

Question 2

amyloidosis

Answer 2

restrictive cardiomyopathy

bright myocardium on echo

Question 3

ank spond

Answer 3

conduction defects, AV block, AR

Question 4

behcets

Answer 4

AR

arterial/venous thrombi

Question 5

beta thalassemia

Answer 5

dialted + restrictive cardiomyopathy

Question 6

carcinoid syndrome

Answer 6

TR

PS

Question 7

downs syndrome

Answer 7

ASD

VSD

MR

Question 8

E-D syndrome

Answer 8

MVP

aortic aneurysm + dissection

hyperelastic skin

GI bleeds

loose hypermobile joints

Question 9

friedrich’s ataxia

Answer 9

hypertrophic cardiomyopathy

dilation over time

Question 10

haemochromatosis

Answer 10

AF

cardiomyopathy

Question 11

holt oram syndrome

Answer 11

ASD

VSD

upper limb defects [polydactyly]

Question 12

HIV

Answer 12

myocarditis

dilated cardiomyopathy

effusion

ventricular aneurysm

SBE/IE

RVF

RVF [pulm htn]

Question 13

hypothyroidism

Answer 13

sinus brady

low pulse pressure

pericardial effusion

CAD

Question 14

kawasaki

Answer 14

coranry arteritis similar to PAN

commoner than rheum fever as a cause of acquired cardiact disease

Question 15

kleinfelters [male]

Answer 15

ASD

psychopathy

learning difficulties

small testes

sparse facial hair

Question 16

marfans

Answer 16

MVP

AR

aortic dissection

look for long fingers + high arched palate

Question 17

myotonic dystrophy

Answer 17

progressive conduction system disease

arrhythmias

Lv dysfunction

Question 18

noonan syndrome

Answer 18

ASD

PS

low set ears

Question 19

polyarteritis nodosa [PAN]

Answer 19

small + medium vaculitis

angina

MI

arrhythmias

CCF

pericarditis

conduction defects

Question 20

RA

Answer 20

conduction defects,

pericarditis

LV dysfunction

AR

coronary arteritis

Question 21

sarcoidosis

Answer 21

av block from infiltrating granulomas

VT/SVT

myocarditis

CCF

restrictive cardiomyopathy

Question 22

syphillis

Answer 22

myocarditis

ascending aortic aneurysm

Question 23

SLE

Answer 23

pericarditis/effusion

myocarditis

MVP

Question 24

systemic sclerosis

Answer 24

pericarditis

pericardial effusion

conduction defects

cardiomyopathy

Question 25

thyrotoxicosis

Answer 25

high pulse AF emboli wide pulse pressure loud heart sounds Ejection systolic murmur angina high output cardiac failure

Question 26

turner syndrome

Answer 26

coA look for webbed neck

Question 27

williams syndrome

Answer 27

supravalvular AS