General JIA

Question 1

ACR Criteria

Answer 1

1. Age of onset <16
2. Arthritis (swelling or effusion, or presence of two or more of the following signs: limitation of ROM, tenderness or pain on motion, or increased heat) in one or more joints
3. Duration: 6 weeks or longer
4. Onset type defined in the first 6 months
   - Poly >=5 joints
   - Oligo <5
   - sJIA
5. Exclusion of other types

Question 2

EULAR Criteria

Answer 2

1. Age of onset <16
2. Arthritis in one or more joints
3. Duration: 3 months
4. Typically defined by characteristics at onset
   - Poly RF neg
   - Poly F positive
   - Oligo
   - Systemic
   - JAS
   - Psoriatic

Question 3

ILAR

Answer 3

1. Age of onset <16
2. Duration: 6 weeks or longer
3. Onset type defined in the first 6 months
   - Poly RF neg
   - Poly F positive
   - Oligo persistent
   - Oligo extended
   - Systemic
   - ERA
   - Psoriatic
   - Undifferentiated

Question 4

Chromosomal abnormalities associated with chronic arthritis

Answer 4

• trisomy 21
• 22q11.2 deletion (Digeorge)
• Turner
• IgA def and deletion of short arm of chromosome 18

Question 5

Brown Syndrome

Answer 5

Tenosynovitis of the superior oblique tendon of the eye leading to pain an loss of upward gaze, sometimes with diplopia

Question 6

Age of onset of sJIA/ sex ratio

Answer 6

1-5 years; Equal

Question 7

Age of onset of oligo/sex ratio

Answer 7

1-3/ 3:1 female

Question 8

Age of onset poly RF neg/sex ratio

Answer 8

Biphasic 1-3 then late childhood/adolescence
Young onset 3:1
Adolescent onset 10:1

Question 9

Age of onset poly RF positive/sex ratio

Answer 9

9-11 years of age/4-13:1

Question 10

Psoriatic onset/sex ratio

Answer 10

Biphasic: preschool then mid to late childhood

60 percent female

Question 11

ERA onset/sex ratio

Answer 11

10-13 years/ male predominant

Question 12

Overall sibling recurrence risk

Answer 12

15

Question 13

RF positive poly gene

Answer 13

HLA DRB1*0401

Question 14

Oligo JIA gene

Answer 14

HLA DRb1*0801, 1101, 13

Question 15

Objective arthritis

Answer 15

Swelling
Warmth
Erythema 
Limited ROM 
Tenderness

Question 16

CHAQ

Answer 16

Child Health Assessment Questionnaire
Two indices
1- Disability (dressing, grooming, eating, walking, hygiene
2- Discomfort (visual analogue scale)

Question 17

JAFAS

Answer 17

Juvenile Arthritis Functional Assessment Scale–> Observer based
Times performance on 10 tasks

Question 18

Jafar

Answer 18

Juvenile Arthritis Functional Assessment Report
Completed by patient or parent
23 items to assess ability to perform tasks

Question 19

Juvenile Self report Index

Answer 19

Specific focus on physical activity in children older than 8

Question 20

JAQq

Answer 20

JIA Quality of Life Questionnaire
4 Dimensions
Gross motor, fine motor, psychosocial function and general sx

Question 21

CAHP

Answer 21

Childhood arthritis Health profile
Parent report, self administered
3 modules: generic health, JIA specific, patient characteristics

Question 22

QolMQ

Answer 22

Quality of My Life Questionnaire

Distinguishes from disease difficulties and generic difficulties

Question 23

Which classification criteria includes IBD?

Answer 23

EULAR