further issues in cystic fibrosis

Question 1

does CF cause fertility issues in men?

Answer 1

yes > 95% are in fertile because of a blocked or absent vas deferens

Question 2

are women with CF fertile?

Answer 2

yes, although poor nutrition may affect chances of conception

Question 3

what steps must be taken before a women with CF becomes pregnant?

Answer 3

careful planning
screening partner
counselling for long term impact
optimum health

Question 4

when are cf patients eligable for lung transplantation?

Answer 4

when FEV1 is <30%
when there i significant weight loss
when there is hypoxia at rest and de saturation on exercise
hypercapnic
worsening QoL
recurrent worsening sepsis

Question 5

when is lung transplantation contriindicated in cf patients?

Answer 5

with other organ failure
malignancy within 5 years
significant peripheral vascular disease 
drug/nicotine or alcohol dependency
active systemic infection
microbiological issues