Ebsteins

Question 1

Ebsteins tricuspid septal displacement should be

Answer 1

At least 8 mm/ m2

Otto gives an absolute value of more than 1 cm

Feigenbaum gives absolute value of more than 2cm😆. But also gives 8mm/m2

Question 2

Associated Left heart disease in Ebsteins

Answer 2

1. LV Non compaction
2. LV Diastolic dysfn
3. MVP
4. LV systolic dysfn(<10% pts)

Paradoxical septal motion makes EF by M mode difficult. So use Simpsons

Question 3

RVOT mechanisms in Ebsteins

Answer 3

1.ATL obstructing the RVOT

Or

2.PS or Pulmonary atresia

Question 4

RVOT in Ebsteins

Answer 4

Dilated compared to Aorta in PSAX

Question 5

The most severe displacement of Ebsteins occurs in which plane

Answer 5

Posterior plane (Septal and PTL)

Question 6

Ebsteins anomaly is due to

Answer 6

Failure of delamination of TV leaflets from IVS

Question 7

SAIL like ATL means

Answer 7

Tethering plus restricted mobility of the leaflet

Question 8

If area of the functional RV is less than …….. it indicates a poor prognosis in Ebsteins

Answer 8

Less than 1/3 rd of Total RV