Congenital Flashcards
Relation of Normal PA to Aorta
ALS- Anterior,left, Superior; PALS - pulmonary artery is ALS
Mitral pulmonary continuity is seen in
TGA
—- has double conus
DORV
Ostium secundum is formed in septum
Primum;
Ostium primum is at lower end of Septum primum
Limbus is formed by Septum—
Secundum.
So will be on RA side
Floor of fossa ovalis is formed by
Septum Primum
Remnant of foremen ovale on the right side is called Fossa ovalis
In coarctation resting arm leg gradient >______is considered if more than
20 mm Hg at rest
After exercise > 40 mm Hg is abnormal
What percentage of cases both subclavians arise after coarctation
3-4%
So BP in all limbs will be equal
Rib notching I coarctation
Notching of posterior 1/3 of 3-8th ribs
Indication for coarctation intervention in children is
peak INSTANTANEOUS gradient more than
20 mm Hg
Role of balloon angioplasty in coarctation
- Balloon angioplasty is an alternative to surgical repair for “older infants & young children”(greater than four months) with native discrete coarctation
- Stent placement has replaced balloon angioplasty as the procedure of choice in “older children and adults “with native coarctation.
- It remains the preferred intervention for all patients with isolated recoarctation regardless of age
Stent placement is not preferred in coarctation if body weight is
Less than 25
The features of REcoarctation absent in children
Hypertension and Headaches are usually absent
Indications for intervention in re coarctation
- Hypertension
- Instantaneous gradient more than 20
- Presence of collaterals
Balloon angioplasty vs Surgery in coarctation risks
Aneurysm and re coarctation more with balloon
Indications for Pulmonary valve replacement
RF>25% measured by CMR
and 2 or more of
RV volume criteria(3 in no); EF, RVOT aneurysm
or Clinical criteria of exercise intolerance,HF,Syncope,sustained VT
ASD may be closed if PVR is
Less than 5 Woods unit
Others the efficacy is uncertain
If Pulmonary artery pressure >2/3 of Systemic pressure should not do
Largest TV leaflet in Ebsteins is
ATL
Called ‘SAIL LIKE’
Indications for surgery in Ebsteins
Cyanosis- spo2-<90%
RV failure….(to be refined)
Deteriorating exercise capacity
Embolism
REC- RV failure, Embolism, Exercise, Cyanosis
Precautions with Venous P valve for PR
Upsize by 3-4 mm
Check for LMCA occlusion with balloon occlusion of RVOT -RAO caudal and lateral views
Deploy proximal part of stent fast to avoid hypotension
Murmur of moderate VSD is evident………..days of birth
Within 2-3 days
Katz Wachtel phenomenon is
Large biphasic QRS in V2-4.
QRS 50 mm or more
Due to biventricular hypertrophy