Deafness in children

Question 1

What are congenital causes of conductive hearing loss in children?

Answer 1

• Anomalies of pinna, external ear canal, drum or ossicles

- congenital cholesteatoma

Question 2

What are autosomal dominant congenital causes of sensorineural hearing loss?

Answer 2

waardenburg
klippel-feil
alport

Question 3

What are autosomal recessive congenital causes of sensorineural hearing loss?

Answer 3

pendred
ushers syndrome
Jerrell and lange-nielsen

Question 4

What are X-linked congenital causes of sensorineural hearing loss?

Answer 4

alports

turners

Question 5

What are infectious congenital causes of sensorineural hearing loss?

Answer 5

CMV
HSV
Syphilis
Rubella
Toxoplasmosis
Group B strep sepsis

Question 6

What are perinatal and postnatal causes of childhood deafness?

Answer 6

anoxia
birth trauma
cerebral palsy 
kernicterus 
meningitis
ototoxic drugs 
lead
skull fracture

Question 7

When is hearing screened in the newborn and how?

Answer 7

within hrs of birth

Otoacoustic emissions

Question 8

What test is done for those w an abnormal otoacoustic emission?

Answer 8

audiological brainstem responses

Question 9

how is hearing tested in children aged 6-18m?

Answer 9

distraction testing - child sits on parents lap and someone in front attracts the Childs attention whilst someone else attempts to distract bu making noises being and beside the child

Question 10

How is hearing tested in children 2-4 yrs?

Answer 10

conditioned response audiometry

speech discrimination

Question 11

How is hearing tested in children 5 yrs?

Answer 11

pure tone audiogram

Question 12

What is possible treatment of childhood deafness?

Answer 12

cochlear implant

Question 13

What is conservative treatment of childhood deafness?

Answer 13

Encourage parents to talk to child as much as possible
educated at another school
arrangements for fitting hearing aids