Congenital Lung Disease

Question 1

Most common congenital EA/TEF

Answer 1

Type C = EA with distal TEF

Question 2

Workup and tx for congenital EA/TEF

Answer 2

Include Echo to look for R side arch, tx R thoracotomy, extrapleural dissection, primary anastomosis

Question 3

Homogenous echogenic mass with systemic arterial supply on prenatal US

Answer 3

Sequestration

Question 4

Treatment of sequestration

Answer 4

Symptomatic or intralobar - surgery, often lobe, control blood supply first

Question 5

Workup for sequestration

Answer 5

Prenatal US. If ELS, a/w vetebral/chest wall anomalies, CDH

Question 6

Large bubble on neonatal cxr

Answer 6

CCAM/CPAM - LLL
CLE - Upper lobe

Question 7

Prognosis of CPAM depends on

Answer 7

Size - midline shift/compression of airway/esophagus

Question 8

Treatment of CPAM/CCAM

Answer 8

Symptomatic - urgent resection; asymptomatic - elective resection at 3-12m old (lobectomy)

Question 9

Differentiate CCAM from CLE

Answer 9

CLE - LUL, CCAM LLL

Question 10

Workup/treatment of CLE

Answer 10

Echo - a/w CHD 14%; asymptomatic may regress, symptomatic - surgery (lobectomy), avoid PPV & may do selective intubation

Question 11

CLE vs acquired lobar emphysema

Answer 11

CLE LUL, acquired is RLL involvement (preterm infants with barotrauma)