Congenital Heart Disease Flashcards
what are the 2 extra connections in a fetal heart that close after birth
- patent foramen ovale: passage between atria, R to L shunt from high O2 right side to left side
- ductus arteriosus: connects pulmonary artery to aorta, shunting blood away from the pulmonary bed to the body
Why do the PFO and DA eventually close after birth
because L sided pressure is higher than R sided after breathing and systemic vascular resistance increases
What is the time frame in which the PFO and the DA close
PFO: within 6 months (due to the loss of R sided pressure)
DA: within 2-3 days (due to L-R pressure change & ecrease in prostaglandins from mom)
Describe some risk factors for CHD
- prematurity
- family history
- genetic syndromes
- maternal factors (DM, HTN, obesity, thyroid, connective tissue, epilepsy, substances)
- fertility (assisted reproductive therapy)
- in utero infection (CMV, rubella, etc)
When is a standard OB ultrasound done with cardiac windows
18-22 weeks
- evaluates outflow tract and 4 chambers
- not all lesions identifiable
- does not evaluate rhythm or function yet
- can proceed to fetal echo if higher risk of CHD
Describe cyanotic CHD
lesions that allow circulation of deoxygenated blood into systemic circulation via intracardiac or extracardiac shunting
Describe ductal-dependent CHD
dependent upon a patent ductus arteriosus to supply pulmonary or systemic blood floow or to allow adequate mixing between parallel circulations
Describe critical CHD
refers to lesions requiring surgery or catheter based interventions in the 1st year of life
List some acyanotic CHD
- atrial septal defect
- ventricular septal defect
- patent ductus arteriosus
- coarctation of the aorta
List some cyanotic CHD
- truncus arteriosus
- HLHS
- tetralogy of fallot
- total anomalous pulmonary venous return
- transposition of great vessels
Describe some physical manifestations of hypoperfusion
- cold extremities
- cyanotic
- poor cap refill
- tachy
- metabolic acidosis
What is ECMO
extracorporeal mechanical oxygenation
- pulmonary bipass
- does job of the lungs
- kids waiting for emergent CHD repair can sit on ECMO for days
Describe cardiogenic shock
circulatory failure
- tissue hypoxia d/t reduced oxygen delivery and/or increased oxygen consumption or inadequate utilization
Can kids with VSD, ASD, and PDA participate in sports?
Yes, with rare exceptions, as long as hemodynamically insignificant
What is the average O2 sat in utero
60%