congenital/developmental disease Flashcards

0
Q

DDH is a spectrum

A

acetabular dysplasia
hip instability
hip dislocation

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1
Q

major risk factors to developmental hip dysplasia

A

packed uterus
breech pregnancy
first born, twin, oligohydraminos

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2
Q

natural hx of neonatal infants

A

DDH is asx so we need

  • screening and reduction
  • ultrasound to measure the angle depth of the acetabulum
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3
Q

screening and reduction tests

A

ortolani

barlow

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4
Q

ortolani

A

abduct hip and push it back in

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5
Q

barlow

A

push hip out

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6
Q

infants and DDH

A

after 2-3 months soft tissues tighten and so the baby shows limited hip abduction on one side (assym) relative to the other

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7
Q

good sign for DDH in infants

A

assymmetric hip and thigh folds

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8
Q

other signs that say DDH

A
thigh shortening (1<other)
Galeazzi or Allis sign
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9
Q

signs of DDH in ambulatory (walking) children

A

leg-length discrepancy if one hip is dislocated
lumbar lordosis if the dislocation is bilateral
limp or waddling gait

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10
Q

Tredelenburg sign

A

pelvis drops when lifitng foot off the floor; virtually shortened femur on affected side

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11
Q

xray sign of DDH in ambulatory children

A

decrease in ossificaiton of femoral head (small/absent ossific nucleus) because its displaced and thus getting decreased nutrition
–we expect the normal femur to align with a vertical shenten line

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12
Q

untreated ddh in older children/younger adults

A

limping w/o pain in childhood
relative weakness in one/both legs
severe osteoarthritis early in life (30s)
only tx hip replacement

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13
Q

goal of tx in DDH

A

early detection and reduction in dysplasia; when reducing it be careful not to cause avascular necrosis

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14
Q

methods (in order that you should try them)

A
Pavlik Harness
Abduction brace
Closed reduction and spica cast
open reduction
other
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15
Q

pavlik harness

A

persistant ortolani maneuver; everytime the baby kicks it pushes its femur into the acetabulum
–wearing it for 12 weeks will cure the baby, but it’s inconvenient and can rarely produce femoral nerve palsy or avascular necrosis, so we need to readjust the harness weekly and check

16
Q

abduction brace

A

used for older kids or if harness didnt work

17
Q

closed reduction and spica cast

A

when harness/brace fail

18
Q

closed reduction

A

when all else fails

19
Q

other methods

A

traction, swaddling

20
Q

clubfoot has three deformity components

A
ankle equinus (plantar flexion)
heel varus (heel rotation to midline)
forefoot adduction
21
Q

clubfoot is associated with

A

amniotic band syndrome
arthrogryposis
larsen’s syndrome
myelomeningocele

22
Q

natural history of clubfoot

A

foot, calf, and leg are smaller and shorter than average

untreated cluvfoot itself is not painful but no treatement can lead to significant deformed painful feet

23
Q

tx clubfoot

A

nonsurfical: ponseti cast

alacarte surgery post ponseti

24
Q

pain in club foot

A

position of foot doesnt cause pain, but can lead to arthreitis with use–>pain

25
Q

ponseti cast

A

long term casting/bracing of the clubgoot in a series before surgery vs other approaches that use it for shorter time period

doesnt work for 5% clubfeet, we need to do full corrective surgery

26
Q

surgery post ponseti

A

up to 15% of ponseti corrected club feet may need tibilias anterior tendon transfer

27
Q

other techniques

A

french technique
surgery
CAVE-carve adductus, varus equinos