congenital/developmental disease Flashcards
DDH is a spectrum
acetabular dysplasia
hip instability
hip dislocation
major risk factors to developmental hip dysplasia
packed uterus
breech pregnancy
first born, twin, oligohydraminos
natural hx of neonatal infants
DDH is asx so we need
- screening and reduction
- ultrasound to measure the angle depth of the acetabulum
screening and reduction tests
ortolani
barlow
ortolani
abduct hip and push it back in
barlow
push hip out
infants and DDH
after 2-3 months soft tissues tighten and so the baby shows limited hip abduction on one side (assym) relative to the other
good sign for DDH in infants
assymmetric hip and thigh folds
other signs that say DDH
thigh shortening (1<other) Galeazzi or Allis sign
signs of DDH in ambulatory (walking) children
leg-length discrepancy if one hip is dislocated
lumbar lordosis if the dislocation is bilateral
limp or waddling gait
Tredelenburg sign
pelvis drops when lifitng foot off the floor; virtually shortened femur on affected side
xray sign of DDH in ambulatory children
decrease in ossificaiton of femoral head (small/absent ossific nucleus) because its displaced and thus getting decreased nutrition
–we expect the normal femur to align with a vertical shenten line
untreated ddh in older children/younger adults
limping w/o pain in childhood
relative weakness in one/both legs
severe osteoarthritis early in life (30s)
only tx hip replacement
goal of tx in DDH
early detection and reduction in dysplasia; when reducing it be careful not to cause avascular necrosis
methods (in order that you should try them)
Pavlik Harness Abduction brace Closed reduction and spica cast open reduction other
pavlik harness
persistant ortolani maneuver; everytime the baby kicks it pushes its femur into the acetabulum
–wearing it for 12 weeks will cure the baby, but it’s inconvenient and can rarely produce femoral nerve palsy or avascular necrosis, so we need to readjust the harness weekly and check
abduction brace
used for older kids or if harness didnt work
closed reduction and spica cast
when harness/brace fail
closed reduction
when all else fails
other methods
traction, swaddling
clubfoot has three deformity components
ankle equinus (plantar flexion) heel varus (heel rotation to midline) forefoot adduction
clubfoot is associated with
amniotic band syndrome
arthrogryposis
larsen’s syndrome
myelomeningocele
natural history of clubfoot
foot, calf, and leg are smaller and shorter than average
untreated cluvfoot itself is not painful but no treatement can lead to significant deformed painful feet
tx clubfoot
nonsurfical: ponseti cast
alacarte surgery post ponseti