Congenital - Cyanotic CHD

Question 1

Give 3 S/S of cyanotic CHD

Answer 1

• cyanosis
• hyperventilating
• delayed growth
• tachycardia
• sweating

Question 2

Ao arises from morphologic RV, PA arises from morphologic LV

Answer 2

Complete transposition of the great arteries (D-TGA)

Question 3

What happens if there is no shunt present with a D-TGA?

Answer 3

It would be fatal

Question 4

Most common cyanotic heart defect

Answer 4

Tetralogy of Fallot

Question 5

4 anomalies of ToF

Answer 5

1. VSD
2. Pulmonary stenosis
3. Overriding Ao
4. RVH

Question 6

Single large vessel arising from the base of the heart

Answer 6

Truncus arteriosus

Question 7

How many different configurations of truncus arteriosus are there?

Answer 7

4

Question 8

PVs drain directly or indirectly into the RA, no connection to LA at all

Answer 8

Total anomalous pulmonary venous return

Question 9

What happens if there is no ASD or PFO (shunt) with TAPVR?

Answer 9

Death

Question 10

Congenital absence/closure of valve. Usually pulmonary or tricuspid

Answer 10

Valvular atresia

Question 11

Is tricuspid atresia shunt dependent?

Answer 11

Yes

Question 12

Most severe end of spectrum of ToF

Answer 12

Pulmonary atresia with VSD

Question 13

Very small LV, Ao stenosis/atresia, MV atresia

Answer 13

Hypoplastic LV

Question 14

Both great arteries come from morphologic RT heart

Answer 14

Double outlet RV

Question 15

Luminal narrowing of the Ao and often associated with bucuspid AV

Answer 15

Coarctation