Clinical Features and Management of Restrictive Lung Diseases Flashcards

1
Q

Name causes of restriction

A
  • Interstitial lung disease: DAD, sarcoidosis, CHP, IPF
  • Pleura: effusion, pneumothorax, thickening
  • Nerve/muscle: amyotrophic lateral sclerosis (motor neurone disease)
  • Bone: Kyphscoliosis, ankylosing spondylitis, rib fractures
  • Others: obesity, pregnancy
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2
Q

Describe the investigation of sarcoidosis

A
  • PFT, WBC, U&E, ECG, TB skin test/eye exam
  • Bronchoscopy including transbronchial biopsy and EBUS
  • CT
  • Surgical biopsy maybe
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3
Q

Describe the clinical management of sarcoidosis

A
  • Mild: no treatment
  • Arthralgia, erythema: NSAIDs
  • Skin lesions, cough: topical steroids
  • Cardiac, neurological, optic, hypercalcaemia: systemic steroids
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4
Q

Describe the clinical management of idiopathic pulmonary fibrosis

A
  • Median survival 3 years
  • Refer to ILD clinic
  • Palliative care
  • Oral anti-fibrotic
  • Perfinodone (pyridone)
  • Nintedanib (kinase inhibitor)
  • Lung transplant
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