Clinical Features and Management of Restrictive Lung Diseases Flashcards
1
Q
Name causes of restriction
A
- Interstitial lung disease: DAD, sarcoidosis, CHP, IPF
- Pleura: effusion, pneumothorax, thickening
- Nerve/muscle: amyotrophic lateral sclerosis (motor neurone disease)
- Bone: Kyphscoliosis, ankylosing spondylitis, rib fractures
- Others: obesity, pregnancy
2
Q
Describe the investigation of sarcoidosis
A
- PFT, WBC, U&E, ECG, TB skin test/eye exam
- Bronchoscopy including transbronchial biopsy and EBUS
- CT
- Surgical biopsy maybe
3
Q
Describe the clinical management of sarcoidosis
A
- Mild: no treatment
- Arthralgia, erythema: NSAIDs
- Skin lesions, cough: topical steroids
- Cardiac, neurological, optic, hypercalcaemia: systemic steroids
4
Q
Describe the clinical management of idiopathic pulmonary fibrosis
A
- Median survival 3 years
- Refer to ILD clinic
- Palliative care
- Oral anti-fibrotic
- Perfinodone (pyridone)
- Nintedanib (kinase inhibitor)
- Lung transplant